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A case of Kaposi`s sarcoma associated with Castleman`s disease
( June Hyuck Yim ),( Hyung Jin Park ),( Hye Jin Ahn ),( Tae In Kim ),( Min Kyung Shin ),( Ki Heon Jeong ) 대한피부과학회 2016 대한피부과학회 학술발표대회집 Vol.68 No.1
Castleman``s disease (CD), also known as angiofollicular lymphoid hyperplasia or giant lymph-node hyperplasia, is an unusual form of a lymphoproliferative disorder, and is divided clinically into a solitary and a multicentric form. Development of multifocal CD most commonly occurs in patients with a documented human herpesvirus 8 (HHV-8) infection. HHV-8 is also known as etiologic agent of Kaposi’s sarcoma (KS) and there are some cases of CD coexisted with KS. A 79-year-old female diagnosed as the plasma cell type of CD was referred to our department with numerous skin lesions consisting of confluent, violaceous-colored plaques and nodules on her legs and soles. Histologic examination of the cutaneous lesions was consistent with KS. Herein, we report a rare case of KS associated with multicentric CD.
A case report of rare malignant eccrine spiradenoma
( June Hyuck Yim ),( Tae In Kim ),( Myong Il Bae ),( Nack In Kim ) 대한피부과학회 2015 대한피부과학회 학술발표대회집 Vol.67 No.1
Malignant eccrine spiradenoma (MES) is a rare adnexal tumour derived from cutaneous sweat glands. It usually presents as a small, firm, reddish painful and small solitary nodule. Head and neck are rare locations. MES arises over a prior benign spiradenoma. Clinical behavior is aggressive with a high rate of recurrences and distant metastases. Diagnosis is based on histological findings and treatment must be aggressive from the beginning to achieve the best results. Wide local excision and close follow up are crucial in the management of MES. A 76-year-old female visited our center for mass on the left cheek, which developed about 3 years ago. We removed the mass by local excision. Histologically, the mass consisted of benign eccrine spiradenomas adjacent to carcinomatous area showing nuclear pleomorphism and marked mitotic activity. Here we report a case of MES that arises in a very unusual location.
Phacomatosis pigmentovascularis type IIa
( June Hyuck Yim ),( Tae In Kim ),( Myong Il Bae ),( Nack In Kim ),( Min Kyung Shin ) 대한피부과학회 2015 대한피부과학회 학술발표대회집 Vol.67 No.1
Phacomatosis Pigmentovascularis (PPV) represents a rare cutaneous congenital malformation syndrome, characterized mainly by the presence of capillary malformation and pigmentary nevi. PPV is first classified into five subtypes and then further categorized according to the absence or presence of associated systemic findings as type (a) and (b), respectively. Among them, type II PPV is characterized by nevus flammeus associated with aberrant mongolian spots. A 4-month-old boy presented to our department with erythemato-violaceous patches on the face and anterior trunk and aberrant Mongolian spots on the trunk, buttocks and lower limbs. All patches were said to be present at birth. The boy showed normal mental and physical development without any systemic abnormality. Biopsy specimen obtained from face showed normal epidermis and dilation of small vessels in the papillary dermis. The boy was diagnosed with type IIa Phacomatosis Pigmentovascularis or cesioflammea. We report this case with a review of literature.
Acute generalized exanthematous pustulosis after exposure to lacquer tree vapor
( June Hyuck Yim ),( Hye Jin Ahn ),( Tae In Kim ),( Myong Il Bae ),( Nack In Kim ),( Min Kyung Shin ) 대한피부과학회 2015 대한피부과학회 학술발표대회집 Vol.67 No.1
Acute generalized exanthematous pustulosis (AGEP) is a rare cutaneous rash characterized by the abrupt onset of a generalized pustular rash often accompanied by fever. There is a history of drug use in 90% of the cases. Lacquer contains an allergen, which can cause severe contact dermatitis. Although, AGEP induced by the ingestion of chicken boiled with lacquer have been reported, there is no case of AGEP induced by lacquer tree vapor. Herein, we reported a 57-year-old male patient with nephrotic syndrome who developed AGEP after exposure to lacquer tree vapor. The patient was referred because of fever and erythematous pustular lesions on the body and extremities. Biopsy specimen from the pustular lesion showed subepidermal seperation of epidermis and infiltration of lymphocytes and neurtophils at dermal papillae and epidermis. Spontaneous resolution was observed 14days after despite maintaining his medication due to his chronic illness.
( June Hyuck Yim ),( Hyung-jin Park ),( Hye-jin Ahn ),( Ki Heon Jeong ),( Min Kyung Shin ),( Mu-hyoung Lee ) 대한피부과학회 2016 대한피부과학회 학술발표대회집 Vol.68 No.2
Background: Treatment of atopic dermatitis (AD) and psoriasis requires their differentiation from other eczematoid dermatitis and a determination of disease severity. However, both can be clinically difficult and the findings subjectively interpreted. Objectives: We investigated the utility of in vivo autofluorescence (AF) measurements for diagnosis of both diseases, and determination of severity. Methods: 30 patients with AD and 30 with psoriasis were recruited, together with sex- and age-matched patients with healthy skin. AF intensity was measured using the EcoSkin® fluorescence video dermatoscope. In AD and psoriasis patients, AF in non-sun-exposed lesional and non-lesional skin was measured. To identify the locations that reflect characteristics of AD, AF was also measured at the other sites in the patients with AD. Results: AD was associated with lower AF and psoriasis with higher AF intensity peaking around 620 nm. In addition, skin AF intensity of each disease was associated with severity of lesion. Conclusion: Non-invasive measurement of skin AF in vivo can aid in diagnosis of AD and psoriasis as well as in treatment monitoring.
( June Hyuck Yim ),( Min Jae Gwak ),( Myong Il Bae ),( Boo Kyoung Kang ),( Ki Heon Jeong ),( Min Kyung Shin ),( Mu Hyoung Lee ) 대한피부과학회 2014 대한피부과학회 학술발표대회집 Vol.66 No.2
Background: Confluent and reticulated papillomatosis (CRP) is an uncommon dermatosis that affects young individuals and presents with greyish papules that coalesce to form a peculiar reticulated pattern usually on the trunk. Histological findings show hyperkeratosis, papillomatosis and some acanthosis, resembling the histological pattern of acanthosis nigricans (AN). AN is clinically characterized by patches or plaques with a greyish papillomatous texture, typically localized on the neck and in intertriginous areas such as the axillae and groin. Objectives: The pathogenesis of CRP and AN is still unknown, CRP and AN are considered as two distinct pathologies and differentiated because of their distinctiveclinical features, but sometimes it is not easy to distinguish these two disease. Methods: Eleven subjects with initially ambiguous diagnosis of CRP or AN were included in our study. Some cases were hard to diagnose exactly, moreover, some cases were considered coexistence of two diseases, although two diseases show different clinical and histopathological findings. So we tried oral minocycline to patients for diagnostic therapy. Results: By the therapeutic response to minocycline, 4 cases were supposed to be as CRP concurrent with AN, 4 cases as CRP, and 3 cases as AN. Conclusion: In conclusion, we consider that the trial of oral minocycline helps to differentiate CRP from AN.
( June Hyuck Yim ),( Tae In Kim ),( In Jung Kang ),( Ki Heon Jeong ),( Su Kang Kim ),( Joo Ho Chung ),( Min Kyung Shin ),( Mu Hyoung Lee ) 대한피부과학회 2014 대한피부과학회 학술발표대회집 Vol.66 No.2
Background: Numerous studies have investigated the potentialrelationship of human leukocyte antigen (HLA)-G 14bp insertion/deletion (INS/DEL) polymorphism with autoimmune disease (AID). However, results from published data were inconclusive. Objectives: Our aim in this study was to determine whether the 14bp INS/DEL polymorphism in the HLA-G gene contributes to the risk of AID. Methods: A systemic literature search of PubMed and Embase databases was conducted to identify eligible studies investigating the association of HLA-G 14bp INS/DEL polymorphism with AID. The final analysis included 13 publications with a total of 6462 individuals. Results: Overall, no significant association between HLA-G 14-bp INS/DEL polymorphism and overall AID was detected in all comparison models. Further subgroup analyses based on AID types and ethnicity showed no significant association. Conclusion: Our results suggest that the HLA-G 14bp INS/DEL polymorphism might not be related to the development of AID. Further studies with larger sample size are warranted to validate our finding.
A case of plexiform neurofibroma developed under the overlying giant cafe-au-lait macules
( June Hyuck Yim ),( Hye Jin Ahn ),( Tae In Kim ),( Myong Il Bae ),( Mu Hyoung Lee ),( Ki Heon Jeong ) 대한피부과학회 2015 대한피부과학회 학술발표대회집 Vol.67 No.1
Neurofibromatosis (NF) is characterized by multiple cafe-au-lait spots, axillary and inguinal freckling, multiple discrete dermal neurofibromas or plexiform neurofibroma, and iris Lisch nodules. Among them, plexiform neurofibroma occurs in only 5 percent of patients with NF type 1. Although characteristically benign, plexiform neurofibromas can cause pain, disfigurement and functional changes and more importantly may turn malignancy. We present a case of a 12-year-old girl with bean-sized nodules under the overlying light brown-colored macule on her left thigh. On physical examination, patient also have more than 6 cafe-au-lait macules (CALM) larger than 5mm in greatest diameter and freckling in the axillary region. By virtue of the presence of CALM and intertriginous freckling, the patient met diagnostic criteria for NF1. Biopsy specimen obtained from nodule under the overlying giant CALM showed plexiform neurofibroma.