성인에서 발생한 터어키안 상부 Atypical Teratoid/Rhabdoid Tumor -증례보고- = Suprasellar Atypical Teratoid/Rhabdoid Tumor：Report of an Adult Case

다국어 초록 (Multilingual Abstract)

Atypical teratoid/rhabdoid tumor(AT/RT) of the central nervous system is a rare and extremely aggressive malignancy, mostly found in early childhood and the posterior fossa appears to be a common location for AT/RT. We report a case of suparsellar AT/RT in an adult patient. A 19-year-old man was admitted with decreased visual acuity and visual field defects for three years. Magnetic resonance image showed a heterogenously enhancing multiseptated mass in the suprasellar area and thickened pituitary stalk. A gross total resection was performed by the subfrontal translamina terminalis approach. Histological diagnosis revealed it as an atypical teratoid/rhabdoid tumor. Local radiotherapy in the suprasellar region was given with total dose of 5400cGy in 27 fractions. The patient has attended regular follow-ups and took hormonal medications without the recurrence of tumor for one year after the surgery.