Russell-Silver 증후군 환아에서 성장 호르몬의 치료효과 = Growth Hormone Therapy in Russell-Silver Syndrome

다국어 초록 (Multilingual Abstract)

Russell-Silver syndrome is characterized by low birth weight, growth retardation, delayed bone age, asymmetry, abnormal sexual development, cranio-facial disproportion, short little finger and clinodactyly. Short stature is the major concern, so there have been interests treating Russell-Silver syndrome with human growth hormone. However, there are no large-scale controlled studies to confirm the effectiveness of growth hormone therapy until now because of the rarity of this disorder. In Korea, we cannot find reports dealing with growth hormone treatment in Russell-Silver syndrome. We present three children with Russell-Silver syndrome who showed accelerated growth with growth hormone treatment.

국문 초록 (Abstract)

자궁내 성장 부전의 가장 심한 형태인 Russell-Silver 증후군에서 가장 문제가 될 수 있는 것이 저신장증이다. 저자들은 Russell-Silver 증후군으로 진단받은 세 명의 환아에게 성장 호르몬 치료 효과를 경험을 하였기에 보고하는 바이다.

참고문헌 (Reference)

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