증례 : 소화기 ; 거대한 간 종괴로 재발한 저 위험도 위장관 간질 종양 1예 = Case Reports : Gastroenterology ; A Case of Huge Hepatic Recurrence of Low Risk Gastrointestinal Stromal Tumor

국문 초록 (Abstract)

위장관 간질종양(GIST)은 저 위험군의 경우 재발은 극히 드물다고 알려져 있다. 저자들은 8년 전 위의 저 위험도 간질종양을 진단받고 근치적 절제술을 시행받은 환자에서 간우엽 전체를 차지하는 거대한 간 종괴로 내원하여 간에 국한된 위장관 간질 종양의 재발을 진단하였기에 문헌고찰과 함께 보고하고자 한다. 이와 같은 위장관 간질 종양의 재발환자는 그 예후가 좋지 않기 때문에 첫 진단 당시 저위험군 환자라 하더라도 근치적 절제술 후 지속적인 추적관찰을 필요로 한다.

다국어 초록 (Multilingual Abstract)

Gastrointestinal stromal tumors (GISTs) are rare mesenchymal tumors that express c-kit. The majority of GISTs are located in the stomach and small intestine. The tumors are classified into very-low-risk, low-risk, intermediate-risk, and high-risk categories based on size and mitosis activity. The recurrence of low-risk GIST is extremely rare. We report a hepatic recurrence of a low-risk gastric GIST that had been removed completely 8 years earlier, and presented as a huge hepatic mass. Since recurrent GIST has a poor prognosis, regular long-term follow-up must be considered, although the primary GIST was low risk. (Korean J Med 2011;80:203-207)

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