신장의 이상회전과 T2Hemivertebra 를 동반한 선천성 일측폐 발육 부전증 1 예 = A Case of Congenital Agenesis of Left Lung with Malrotation of Both Kidney and T2Hemivertebra

다국어 초록 (Multilingual Abstract)

A case of congenital agenesis of left lung of a 19-years-old female is presented in detail with some review of literature. She had been suffered from mild dyspnea on exertion since early childhood but she was been comfatable unti16 months ago, when frequent upper respiratory infection and dyspnea developed. From 10 days earlier, mild fever was associated and dyspnea on exertion was aggravated.
Her past history and family history were not contributary. Physical examination revealed asymmetrical development of both thoracic cage and showed limited respiratory movement of left thorax. There were increased percussion dullness and absent breathing sounds over entire left lung field except left upper lung field. The cardiac dullness was shifted to the left and heart sunds were heard over the 4th ICS X MCL.
A roentgenogram of the chest revealed shifting to the left of trachea and mediastinum, homosgenou increased density of left lung, hyperlucency of right lung, and T, hemivertebra, Bronchoscopy showed total absence of left main bronchus. Bronchogram revealed above findings too, but right main bronchus was intact.
CT scan revealed agenesis of left lung and herniation of right lung to left hemithorax. Intravenous pyelography showed malrotation of kidney. Pulmonary angioram and cardiac catheterization showed unremarkable findings except total absence of left pulmonary artery.