HWW(Herlyn-Werner-Wunderlich) 증후군은 중복자궁, 일측성 폐쇄질 및 동측 신장 무형성을 보이는 비뇨생식기계의 선천성 기형으로 매우 드문 질환 중 하나이다. 대부분 초경 이후 발생하는 월경통이...
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https://www.riss.kr/link?id=A101470674
김명수 (관동대) ; 박용준 (관동대) ; 박영준 (관동대) ; 박노혁 (관동대학교) ; 송지선 (관동대학교) ; 김병길 (관동대) ; Kim, Myoung-Soo ; Park, Yong-Jun ; Park, Young-Jun ; Park, Noh-Hyuck ; Song, Ji-Sun ; Kim, Pyung-Kil
2007
Korean
KCI등재후보
학술저널
299-305(7쪽)
1
0
상세조회0
다운로드국문 초록 (Abstract)
HWW(Herlyn-Werner-Wunderlich) 증후군은 중복자궁, 일측성 폐쇄질 및 동측 신장 무형성을 보이는 비뇨생식기계의 선천성 기형으로 매우 드문 질환 중 하나이다. 대부분 초경 이후 발생하는 월경통이...
HWW(Herlyn-Werner-Wunderlich) 증후군은 중복자궁, 일측성 폐쇄질 및 동측 신장 무형성을 보이는 비뇨생식기계의 선천성 기형으로 매우 드문 질환 중 하나이다. 대부분 초경 이후 발생하는 월경통이나 복강내 종물등으로 발견되지만, 본 증례는 소아에서 반복되는 요로 감염과 현미경적 혈뇨로 인해 진단된 경우이다. 복부 초음파 검사에서 일측 신무형성이나 중복 자궁의 소경이 보일 때는 이러한 뮬러관 기형의 가능성을 염두에 두어야 보다 빠른 진단이 가능하고, 환자의 고통 또한 중여줄 수 있을 것이다. 특히 반복되는 요로 감염시에도 단순한 감염 치료보다 정밀검사를 항상 염두에 두어야 할 것이다.
다국어 초록 (Multilingual Abstract)
Herlyn-Werner-Wunderlich syndrome(HWWs) is a rare variant of Mullerian ductal anomalies characterized by the presence of a hemivaginal septum, a didelphic uterus, and ipsilateral renal agenesis. It usually presents after menarche with progressive pelv...
Herlyn-Werner-Wunderlich syndrome(HWWs) is a rare variant of Mullerian ductal anomalies characterized by the presence of a hemivaginal septum, a didelphic uterus, and ipsilateral renal agenesis. It usually presents after menarche with progressive pelvic pain, and palpable mass due to hemihematocolpos. If a cystic mass is detected behind the urinary bladder in children, in association with the absence of a kidney, the diagnosis of uterus didelphys with imperforate vagina and hydrocolpos should be considered. When renal agenesis is found in asymptomatic children, the small size and the tubular shape of the uterus makes it almost impossible to evaluate uterine anomalies, so follow-up should be performed until the end of puberty. Appropriate preoperative diagnosis and treatment will prevent unnecessary procedures and offer relief of symptoms. We report one case of didelphic uterus with blind hemivagina and ipsilateral renal agenesis with biopsy- proven thin glomerular basement membrane disease which is not related to the above syndrome.
참고문헌 (Reference)
1 "Urological anomalies in children with renal agenesis or multicystic dysplastic kidney" 47 : 171-176, 2006
2 "Unusual form of genital malformation with aplasia of the right kidney" 559-62, zentralblgynakol1976;98
3 "The congenital and acquired solitary kidney" 5 : 2-8, 2003
4 "Simultaneous occurrence of an open Gartner-duct cyst a homolateral aplasia of the kidney and a double uterus as a typical syndrome of abnormalities" 340-7, geburtshilfefrauenheilkd1971;31
5 "Renal aplasia is the predominant cause of congenital solitary kidneys" 61 : 1840-1844, 2002
6 "Mullerian defects in women with normal reproductive outcome" 1192-3, fertilsteril1991;56
7 "Management and outcome of patients with combined vaginal septum, bifid uterus, and ipsilateral renal agenesis(Herlyn-Werner-Wunderlich syndrome)" 41 : 987-992, 2006
8 "Magnetic resonance imaging in the evaluation of uterus didelphys with obstructed hemivagina and renal agenesis: a case report" 274 : 246-247, 2006
9 "MR imaging diagnosis of uterovaginal anomalies: current state of the art" 23 (23): 2003
10 "Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases" 37 : 657-665, 2007
1 "Urological anomalies in children with renal agenesis or multicystic dysplastic kidney" 47 : 171-176, 2006
2 "Unusual form of genital malformation with aplasia of the right kidney" 559-62, zentralblgynakol1976;98
3 "The congenital and acquired solitary kidney" 5 : 2-8, 2003
4 "Simultaneous occurrence of an open Gartner-duct cyst a homolateral aplasia of the kidney and a double uterus as a typical syndrome of abnormalities" 340-7, geburtshilfefrauenheilkd1971;31
5 "Renal aplasia is the predominant cause of congenital solitary kidneys" 61 : 1840-1844, 2002
6 "Mullerian defects in women with normal reproductive outcome" 1192-3, fertilsteril1991;56
7 "Management and outcome of patients with combined vaginal septum, bifid uterus, and ipsilateral renal agenesis(Herlyn-Werner-Wunderlich syndrome)" 41 : 987-992, 2006
8 "Magnetic resonance imaging in the evaluation of uterus didelphys with obstructed hemivagina and renal agenesis: a case report" 274 : 246-247, 2006
9 "MR imaging diagnosis of uterovaginal anomalies: current state of the art" 23 (23): 2003
10 "Herlyn-Werner-Wunderlich syndrome: uterus didelphys, blind hemivagina and ipsilateral renal agenesis. Sonographic and MR findings in 11 cases" 37 : 657-665, 2007
11 "Genital anomalies associated with solitary kidney" 538-48,
12 "Didelphic uterus and obstructed hemivagina with renal agenesis: case report and review of the literature" 17 : 137-141, 2004
13 "Diagnosing neonatal female genital anomalies using saline-enhanced sonography" 177 : 1041-1044, 2001
14 "Bicervical Bicornuate Uterus with Unilateral Cervial Atresia and Homolateral Renal Agenesis" 12 : 2841-2845, 1999
15 "Asymmetric lateral distribution of obstructed hemivagina and renal agenesis in women with uterus didelphys: institutional case series and a systematic literature review" 87 : 719-724, 2007
16 "Associated urologic anomalies in children with solitary kidney" 39 : 85-87, 2004
17 "Analysis of renal biopsies performed in children with abnormal findings in urinary mass screening" 95 : 849-853, 2006
18 "A new embryologic classification for uro-gynecologic malformations the syndromes of mesonephric duct induced mullerian deformities" 265-7, jurol1979;121
19 "A Case of the Syndrome of Uterus Didelphys, Unilateral Obstructed Hemivagina, and Ipsilateral Renal Agenesis Associated with Ipsilateral Gartner's Duct Cyst and Contralateral Renal Cysts" 41 : 689-693, 2000
20 "A Case of Communicating Double Uterus with Double Cervix, Blind Hemivagina and Ipsilateral Renal Agenesis" 23 : 801-806, 2002
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전신성 홍반성 루프스와 동시 발병한 혈전성 혈소판 감소성 자반증 2예
학술지 이력
연월일 | 이력구분 | 이력상세 | 등재구분 |
---|---|---|---|
2024 | 평가예정 | 계속평가 신청대상 (계속평가) | |
2022-01-01 | 평가 | 등재후보학술지 선정 (신규평가) | ![]() |
2021-12-01 | 평가 | 등재후보 탈락 (계속평가) | |
2019-01-01 | 평가 | 등재후보학술지 선정 (신규평가) | ![]() |
2018-12-01 | 평가 | 등재후보 탈락 (계속평가) | |
2017-12-01 | 평가 | 등재후보로 하락 (계속평가) | ![]() |
2016-01-12 | 학술지명변경 | 한글명 : 대한소아신장학회지 -> Childhood Kidney Diseases외국어명 : Journal of the Korean Society of Pediatric Nephrology -> Childhood Kidney diseases | ![]() |
2013-01-01 | 평가 | 등재 1차 FAIL (등재유지) | ![]() |
2010-01-01 | 평가 | 등재학술지 선정 (등재후보2차) | ![]() |
2009-01-01 | 평가 | 등재후보 1차 PASS (등재후보1차) | ![]() |
2008-01-01 | 평가 | 신청제한 (등재후보1차) | ![]() |
2007-01-01 | 평가 | 등재후보 1차 FAIL (등재후보2차) | ![]() |
2006-01-01 | 평가 | 등재후보 1차 PASS (등재후보1차) | ![]() |
2004-01-01 | 평가 | 등재후보학술지 선정 (신규평가) | ![]() |
학술지 인용정보
기준연도 | WOS-KCI 통합IF(2년) | KCIF(2년) | KCIF(3년) |
---|---|---|---|
2016 | 0.12 | 0.12 | 0.13 |
KCIF(4년) | KCIF(5년) | 중심성지수(3년) | 즉시성지수 |
0.11 | 0.11 | 0.332 | 0 |