The major manifestations of Rieger's syndrome are ocular and dental abnormalities. The ocular abnorma-lities include partial or complete hypoplasia of the iris stroma, the presence of iris strands crossing the angle of the anterior chamber of the eye,...
The major manifestations of Rieger's syndrome are ocular and dental abnormalities. The ocular abnorma-lities include partial or complete hypoplasia of the iris stroma, the presence of iris strands crossing the angle of the anterior chamber of the eye, and the presence of posterior embryotoxon. Hypodontia, microdontia, peg shaped teeth, and malocclusion (bilateral cross-bites) are common oral findings. Hypoplasia of the maxilla causes the mandible to appear prominent.
The authors observed a patient with Rieger's syndrome who was a 13year-old girl. With reserach of literature, the case is presented.