자연기흉으로 발현된 활막육종의 재발 1예 = Recurrent Synovial Sarcoma Manifested as Bilateral Spontaneous Pneumothorax

다국어 초록 (Multilingual Abstract)

Synovial sarcomas' are rare malignant neoplasms that arise from mesenchymal cells of tendosynovial tissue, accounting for about 7% of adult soft tissue sarcomas, and occur with maximal frequency in the second through fifth decades of life. The incidence of metastasis is high, most often to the lung, regional lymph nodes and bone, despite of radical surgery for primary tumor. The histologic subtypes of synovial sarcoma generally accepted are monophasic, biphasic and poorly undifferenciated types, and all synovial sarcomas have been classified as high grade soft tissue sarcoma due to high metastatic potentials by the American Joint Committee on Cancer. Spontaneous pneumothorax due to primary pulmonary neoplasm is uncommon, and pneumothorax due to pulmonary metastasis is very uncommon condition. The most common primary tumor causing spontaneous pneumothorax is sarcoma, and of these the majority are osteosarcomas. Various mechanisms have been suggested to explain how a spontaneous pneumothorax occurs as a result of pulmonary involvement of malignancy. Bilateral spontaneous pneumothorax from pulmonary metastasis of synovial sarcoma has been reported very rarely in the world literature, and has not yet been reported in Korea. We present here a very rare case of recurrent synovial sarcoma manifested as bilateral spontaneous pneumothorax, who had been treated with surgical resection and radiotherapy for the synovial sarcoma on left popliteal fossa and review the pertinent literatures.