Middle Aortic Syndrome with Superior Mesenteric and Bilateral Renal Artery Involvement: Unusual Type of Aortic Coarctation

다국어 초록 (Multilingual Abstract)

Middle aortic syndrome (MAS) is very uncommon vascular pathology characterized by a long segmental narrowing or obstruction of the abdominal and/or distal thoracic aorta, commonly involving with the visceral and renal arteries. This syndrome may be presented with various physical signs of coarctation of the aorta, including resistant hypertension, renal insufficiency and/or mesenteric ischemia. Here, we report a case of a 64-year-old man with severe hypertension. He was diagnosed with MAS associated with stenosis of visceral and renal vessels by use of computed tomography and magnetic resonance angiography.

참고문헌 (Reference)

1 Tosun O, "Unusual congenital aortic anomaly with rare common celiamesenteric trunk variation : MR angiography and digital substraction angiography findings" 30 : 1061-1064, 2007

2 Ilica AT, "Thoracoabdominal aorta coarctation with bilateral renal artery involvement : diagnosis with multidetector CT angiography(MDCTA)" 23 : 645-648, 2007

3 Sen PK, "The middle aortic syndrome" 25 : 610-618, 1963

4 Modrall JG, "Operative mortality for renal artery bypass in the United States: results from the National Inpatient Sample" 48 : 317-322, 2008

5 Kim DK, "Middle aortic syndrome diagnosed at 51 years of age" Korean J Med 293-297, 2004

6 Kim SJ, "Middle aortic syndrome : report of 4 cases" 11 : 230-237, 1995

7 Delis KT, "Middle aortic syndrome : from presentation to contemporary open surgical and endovascular treatment" 17 : 187-203, 2005

8 Terramani TT, "Hypoplasia of the descending thoracic and abdominal aorta : a report of two cases and review of the literature" 36 : 844-848, 2002

9 Celik T, "Hypoplasia of the descending thoracic and abdominal aorta : a case report and review of literature" 21 : 296-299, 2006

10 김정아, "Hypertensive Heart Failure with Severe Arteriosclerotic Stenosis of the Descending Aorta" 대한심장학회 37 (37): 590-593, 2007

11 Textor SC, "Critical perfusion pressure for renal function in patients with bilateral atherosclerotic renal vascular disease" 102 : 308-314, 1985

12 Cohen JR, "Coarctation of the abdominal aorta" 8 : 160-164, 1988