피부근염 환자에서 빠르게 진행한 간질성폐렴 1예 = Rapidly Progressive Interstitial Lung Disease Associated with Dermatomyositis; A Case Report

다국어 초록 (Multilingual Abstract)

A previously healthy 44-year-old woman who was diagnosed as having dermatomyositis suddenly developed severe dyspnea while being in the state of improved condition of muscle weakness. Interstitial lung disease was found on high resolution computed tomography (HRCT). In spite of the treatment with the immune-modulating agent (high dose steroid, cyclophosphamide, immunoglubulin and cyclosporine), her condition deteriorated further and rapidly, leading to death. More intensive agent such as FK506 would be necessary in those cases of dermatomyositis-related interstitial lung disease that have poor prognostic factors.

참고문헌 (Reference)

1 "폐를 침범한 피부근염/다발성근염의 임상적 양상" 51 : 354-363, 2001

2 "염증성 근육병증에 동반된 폐침범의 임상적 특징" 14 : 15-22, 2007

3 "Two distinct clinical types of interstitial lung disease associated with polymyositis-dermatomyositis" 101 : 1761-1769, 2007

4 "Tacrolimus in refractory polymyositis with interstitial lung disease" 22 : 1763-1764, 1999

5 "Polymyositis/dermatomyositis and interstitial lung disease: a new therapeutic approach with T-cell-specific immunosuppressants" 38 : 383-392, 2005

6 "Polymyositis and dermatomyositis" 362 : 971-982, 2003

7 "Interstitial lung disease in polymyositis and dermatomyositis" 17 : 701-706, 2005

8 Fathi M, "Interstitial lung disease in polymyositis and dermatomyositis" 17 : 701-706, 2005

9 "Interstitial lung disease and amyopathic dermatomyositis" 44 : 1282-1286, 2005

10 "Intersitial lung disease in polymyositis and dermatomyositis" 40 : 614-622, 2002

11 "Early assessment of rapidly progressive interstitial pneumonia associated with amyopathic dermatomyositis" 26 : 436-439, 2005

12 "Cyclosporine treatment for polymyositis/dermatomyositis: is it possible to rescue the deteriorating cases with interstitial pneumonitis?" 26 : 24-29, 1997

13 "Corticosteroid resistant interstitial pneumonitis in dermatomyositis/ polymyositis: prediction and treatment with cyclosporine" 26 : 1527-1533, 1999

14 "Activation of pulmonary T cells in corticosteroid-resistant and-sensitive interstitial pneumonitis in dermatomyositis/polymyositis" 129 : 541-548, 2002