Bicuspid Aortic Valve: Unresolved Issues and Role of Imaging Specialists

다국어 초록 (Multilingual Abstract)

Bicuspid aortic valve (BAV) is the most common congenital heart disease with marked heterogeneity in many aspects. Fusionpatterns of the aortic cusp are quite variable with different type and severity of valvular dysfunction. Moreover, non-valvularcardiovascular abnormalities are associated with BAV. Among them, aortic aneurysm/dissection is the most serious clinicalcondition with variable patterns of segmental aortic dilatation. Potential association between BAV phenotype and valvulopathyor aortopathy has been suggested, but needs to be tested further. A lack of long-term outcome data at this moment is responsiblefor unresolved debate regarding appropriate management of patients with BAV, specifically to prevent development of aorticdissection. Long-term follow-up data of a well-characterized cohort or registry based on standardized classification of BAVphenotype and aortopathy are necessary for evidence-based medical practice. Advanced imaging techniques such as computedtomography or magnetic resonance imaging offer better opportunities for accurate phenotype classification and imagingspecialists should play a central role to establish a collaborative multicenter cohort or registry.

참고문헌 (Reference)

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