신경통성 근위축증 = Neuralgic Amyotrophy

다국어 초록 (Multilingual Abstract)

In clinical practice, neuralgic amyotrophy (NA) is being frequently underdiagnosed, and its actual incidence is reported to be 1/1000 cases per year. Here, we present an overview of the essentials on NA. The cause of NA is known to be multifactorial (immunologic, mechanical, or genetic factors). Typically, patients with NA show sudden onset of pain in the shoulder region, followed by patchy flaccid paralysis of the muscles in the upper extremity. NA is suspected based on the clinical history and physical examination. However, prior to confirming the diagnosis of NA, other disorders showing similar clinical presentations with NA, such as cervical radiculopathy or rotator cuff pathology, should be ruled out. Electromyography, nerve conduction study, High-resolution ultrasound and magnetic resonance neurography are useful for confirming the diagnosis and judging the necessity of surgical operation. The prognosis depends on the degree of weakness of muscles innervated by involved nerves and the degree of axonal damage in nerve conduction study. Our review would be helpful for clinicians to diagnose NA and treat the symptoms of NA appropriately.

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