대장에 발생한 림프관종증 1예 = A Case of Lymphangiomatosis Arising in the Colon

다국어 초록 (Multilingual Abstract)

Lymphangioma is a benign vascular lesion that shows the characteristics of subepithelial tumor, which can proliferate in the lymphatic system. Only a few cases of multiple lymphangimas of the colon, the so called “colonic lymphanigomatosis”, have been currently reported on the medical literature. Because lymphangioma is absolutely a benign tumor, it does not require any specific treatment, except for rare disease-related symptoms or complications such as anemia, intussusception and protein-losing enteropathy. Endoscopic resection for this tumor has sometimes been performed for both diagnostic and therapeutic purposes. We recently experienced a case of multiple colonic lymphangomas that arose in the ascending colon of a 46-year-old male patient and these lesions were found during performance of colonoscopy. The final diagnosis was confirmed by a pathologic examination of the specimen that was obtained via endoscopic resection. Follow-up colonoscopy at 1 year after the initial examination showed complete resolution of the previously noted lesions without any specific treatment. We report here on a very rare case of colonic lymphangiomatosis along with a brief review of the relevant literature.

국문 초록 (Abstract)

대장에 발생하는 림프관종은 대부분 단발성으로, 대장 내시경검사가 널리 보급됨에 따라 진단율이 높아지고 있지만, 다발성으로 발생하는 경우는 비교적 드물다. 대부분 증상이 없이 대장 내시경 검사 중 우연히 발견되며 양성 질환으로 악성 변화가 보고된 적이 없어, 무증상일 경우 경과 관찰로 충분하지만 빈혈, 장중첩증, 단백상실성 장병증 등의 합병증을 동반할 때는 내시경적 치료나 수술적 치료를 고려해 볼 수 있다. 저자들은 46세 남자의 대장 내시경 검사에서 다발성 상피하 종양이 관찰되어 내시경 절제술을 이용하여 림프관종증으로 진단하였고, 경과 관찰 중 병변이 모두 소실된 1예를 경험하여 문헌 고찰과 함께 보고한다.

참고문헌 (Reference)

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