복강내 거대 농양으로 발현한 산발 유건종 1예 = A Case of Desmoid Tumor Presenting as Intra-abdominal Abscess

다국어 초록 (Multilingual Abstract)

Desmoid tumor is a rare benign tumor derived from fibrous sheath or musculoaponeurotic structure. The tumor is benign histologically but considered as malignant clinically because it has high propensity on infiltrative growth with local invasion and tendency to recurrence after local excision. Especially, when this tumor happens to be in the intra-abdomen, the prognosis is worse because it can cause intestinal obstruction, ureter obstruction and, fistula formation. It also can invade major vessels in abdomen. This tumor occurs more frequently in patients with familial adenomatous polyposis (FAP), in post-partume women, and at old surgical incision site. However, in this case, the patient had neither previous surgery nor a FAP history. We report a rare case of the young male patient who presented with an acute abdomen and underwent laparotomy and was found to have an intra-abdominal desmoid tumor with abscess formation. (Korean J Gastroenterol 2009;53:315-319)

참고문헌 (Reference)

1 정인두, "가족성 선종성 용종증 수술 후 발생한 복강 내 유건종 1예" 대한소화기내시경학회 33 (33): 50-53, 2006

2 Lee HS, "Unresectable desmoid tumor developing after surgery of F.A.P case report" 14 : 323-329, 1998

3 Bus PJ, "Treatment of mesenteric desmoid tumours with the anti-oestrogenic agent toremifene: case histories and an overview of the literature" 11 : 1179-1183, 1999

4 Reitamo JJ, "The desmoid tumor. I. Incidence, sex-, age- and anatomical distribution in the Finnish population" 77 : 665-673, 1982

5 Smith AJ, "Surgical management of intra-abdominal desmoid tumours" 87 : 608-613, 2000

6 Church J, "Staging intra-abdominal desmoid tumors in familial adenomatous polyposis: a search for a uniform approach to a troubling disease" 48 : 1528-1534, 2005

7 Suit H, "Radiation in the multidisciplinary management of desmoid tumors" 35 : 107-119, 2001

8 Lopez R, "Problems in diagnosis and management of desmoid tumors" 159 : 450-453, 1990

9 Jalini L, "Intraabdominal desmoid tumour presenting with perforation" 4 : 114-116, 2006

10 Cruz-Correa M, "Familial adenomatous polyposis" 58 : 885-894, 2003

11 Risum S, "Doxorubicin treatment of an intra-abdominal desmoid tumour in a patient with familial adenomatous polyposis" 5 : 585-586, 2003

12 Kulaylat MN, "Desmoid tumour: a pleomorphic lesion" 25 : 487-497, 1999

13 Khorsand J, "Desmoid tumors and their management" 149 : 215-218, 1985

14 Cholongitas E, "Desmoid tumor presenting as intra-abdominal abscess" 51 : 68-69, 2006

15 Corbel L, "Desmoid tumor of the mesentery. An uncommon cause of ureteral obstruction" 73 : 669-672, 1992

16 Park BH, "Desmoid tumor and duodenal adenoma in a patient with familial adenomatous polyposis: a case report" 23 : 32-35, 2001

17 Heidemann J, "Antiangiogenic treatment of mesenteric desmoid tumors with toremifene and interferon alfa-2b: report of two cases" 47 : 118-122, 2004

18 Eren S, "A sporadic abdominal desmoid tumour case presenting with intermittent intestinal obstruction" 17 : 285-288, 2007

19 Couture J, "A germline mutation at the extreme 3' end of the APC gene results in a severe desmoid phenotype and is associated with overexpression of beta-catenin in the desmoid tumor" 57 : 205-212, 2000