안면신경마비를 주소로 한 베게너육아종증 = Facial Palsy as a Presenting Symptom of Wegener`s Granulomatosis

다국어 초록 (Multilingual Abstract)

Wegener`s granulomatosis is a serious multi-systemic disease pathologically characterized by necrotizing vasculitis and granuloma. Although nervous system is one of major target organs in Wegener`s granulomatosis, the involvement of facial nerve was rarely reported as an initial symptom. We experienced a female patient with Wegener`s granulomatosis presenting otitis media, sinusitis and right facial palsy. Nasal mucosal biopsy revealed necrotizing vasculitis with granuloma formation, which was consistent with Wegener`s granulomatosis. During steroid and cyclophosphamide therapy, she developed paralysis of abducens nerve. Methyprednisolone pulse therapy was administrated with symptomatic improvement. We describe a case of Wegener`s granulomatosis presenting facial nerve palsy.