두개저와 상부 경추를 침범한 고어햄씨병의 보존적 치료 및 방사선 치료에 대한 경험 -증례보고- = Conservative Management and Radiation Therapy of Gorham`s Disease Involved Skull Base and upper Cervical Spine -Case Report-

다국어 초록 (Multilingual Abstract)

A 10-year-old boy was admitted at our institute with neck pain, limiting the neck movement and chin point deviation to the right. Which confirmed the suspected diagnosis of Gorham`s disease, the patient underwent biopsy on the 3rd cervical spine. Gorham`s disease was confidently diagnosed with the support of present clinical and radiographic findgings by a regional histopathologist. In order to diminish neck pain and ensure radiation field uniformity, a halo-vest was recommended. The patient received 4,000 cGy of radiation to the upper cervical osteolytic lesion. There has been no radiographic evidence of progression of the disease at the MR follow-up of post-radiotherapy 23 months. At present, the patient is remarkably doing well with no evidence of disease progression. The authors suggest that application of a halo-vest and early radiation therapy can be a good choice to management of Gorham`s disease involving skull base and upper cervical spine. However, long term follow-up will be essential to confirm the remission of disease.