누난 증후군 환자에서 정맥마취의 경험 = The experience of the total intravenous anesthesia of patient with Noonan synerome

다국어 초록 (Multilingual Abstract)

Noonan syndrome is a condition involving facial, cardiovascular and skeletal abnormalities that may pose problems to anesthesiologists during surgery. Propofol, which is used as an induction agent for noncardiac surgery, produces little or no change in the heart rate. Remifentanil decreases the sympathetic and somatic responses to noxious stimuli and can be given in high doses without negative inotropic effects. We report successful management of a patient with Noonan syndrome, hypertrophic cardiomyopathy, and atrial fibrillation, undergoing laparoscopic cholecystectomy using the the total intravenous anesthesia with propofol and remifentanil.

참고문헌 (Reference)

1 "Use of remifentanil in a patient with peripartum cardiomyopathy requiring caesarean section" 86 : 135-138, 2001

2 "The use of remifentanil during general anaesthesia for caesarean delivery in two patients with severe heart dysfunction" 11 : 38-43, 2002

3 "The pharmacokinetics of remifentanil" 8 : 679-682, 1996

4 "The Noonan syndrome - a review of the clinical and genetic features of 27 cases. J Pediatr 1973" 941-50,

5 "Regional anesthesia for cesarean section in a parturient with Noonan's syndrome. Anesthesiology 1988" 636-8,

6 "Orthognathic surgery in a patient with Noonan's syndrome. J Oral Maxillofac Surg 1994" 421-5,

7 "Mapping a gene for Noonan syndrome to the long arm of chromosome 12. Nat Genet 1994" 357-60,

8 "Hypertrophic obstructive cardiomyopathy in combination with a prolapsing mitral valve. Anaesthesia for surgical correction with propofol. Anaesthesia 1989" 409-11,

9 "Hypertrophic cardiomyopathy in Noonan syndrome" 38 : 91-98, 1996

10 "Genetic counselling in Noonan syndrome. Am J Med Genet 1993" 437-40,

11 "Epidural anesthesia for cesarean section in patients with hypertrophic cardiomyopathy: a report of three cases" 90 : 1205-1207, 1999

12 "Coagulation-factor deficiencies and abnormal bleeding in Noonan's syndrome. Lancet 1992" 19-21.

13 "Coagulation-factor deficiencies and abnormal bleeding in Noonan's syndrome. Lancet 1992" 19-21.

14 "Clinical anesthesiology. 4th ed" USA, McGraw-Hill 475-, 2006

15 "Anesthetic management of a child with Noonan's syndrome and idiopathic hypertrophic subaortic stenosis. Anesth Analg 1992" 464-6,

16 "Anaesthesia in a patient with Noonan's syndrome and cardiomyopathy. Anaesthesia 1992" 131-3,

17 "A clinical study of Noonan syndrome. Arch Dis Child 1992" 178-83,