영아 연축을 동반한 Krabbe병 1례

김자경,김달현,강보영,권영세,홍영진,손병관,윤혜란,Kim, Ja Kyoung,Kim, Dal Hyun,Kang, Bo Young,Kwon, Young Se,Hong, Young Jin,Son, Byong Kwan,Yoon, Hye Ran 대한소아청소년과학회 2003 Clinical and Experimental Pediatrics (CEP) Vol.46 No.1

저자들은 뇌성마비로 진단받고 치료중 조절되지 않은 경련을 주소로 본과로 전원되어 자기 공명영상 촬영과 효소 측정법으로 Krabbe병의 조기 발현형으로 진단 받은 환자 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다. Krabbe disease is a rare autosomal recessive disorder clinically characterized by retardation in motor development, prominent spasticity, seizures, and optic atrophy. Pathologically, there are many globoid cells in the white matter, in addition to the lack of myelin and the presence of severe gliosis. Hence Krabbe disease is known as globoid cell leukodystrophy. Biochemically, the primary enzymatic deficiency in Krabbe disease is galactocerebroside beta-galactosidase. Patients with Krabbe disease can be subdivided into the early-onset type and late-onset type, according to the onset of clinical manifestations. Most patients with early-onset type die before their second birthday. We describe a girl with Krabbe disease associated with uncontrolled seizures, which was confirmed with biochemical study and MRI. The clinical findings of this patient included hyperirritability, scissoring of the legs, flexion of arm, and clenching of the fists, and generalized tonic seizures. EEG showed hypsarrhythmia, and MRI demonstrated degenerative white matter changes in bilateral periventricular white matter, posterior rim of internal capsule, basal ganglia and brain stem on T2W1 and FLAIR image. The diagnosis was based on clinical features of progressive neurologic deterioration in conjunction with low galactocerebroside beta-galactosidase activity.

해안 가로의 지속가능성 향상을 위한 가로 시설물 연구 - 제주도 해수욕장 주변 가로시설물을 중심으로 -

김자경,Kim, Ja Kyung 한국실내디자인학회 2017 한국실내디자인학회논문집 Vol.26 No.4

In Korea, which has three sides of the sea, various waterfront spaces are being developed and developed along with various coastal landscapes. However, there are a lot of cases that do not consider the regional characteristic of the coast or the characteristic of the coastal landscape. In many cases, the street facilities cause the landscape degradation and the use inconvenience because of incongruity with the scenery, aging and lax management. Therefore, it is necessary to reflect the specificity of the coastal landscape in planning and directing the street facilities, harmonizing with the surrounding natural environment, and consideration of sustainability. However, there is no research or planning index for sustainable street facilities considering the coastal characteristics. Therefore, this study suggests plan elements to improve the sustainability of the street facilities on the shore and proposes them as basic plan elements, and suggests what kind of improvements should be made to improve the sustainability of coastal facilities in Korea. Based on the plan elements derived from the plan, we checked the problems and complementary points of coastal street facilities in Korea by analyzing the current status of the street facilities around the Jeju Island beach from a sustainable point of view, and suggested plan indicators that should be supplemented to improve sustainability. We surveyed the street facilities such as walkway blocks, benches, pagoda, drinking fountain, trash cans, bicycle shelters, fences, guide maps, streetlights, and shower rooms in 10 beaches in Jeju Island. This study analyzed the sustainability characteristics of the each factor of these facilities by surveying the reflectivity of the 23 plan indicators from the six aspects derived from the sustainability planning factor as conformity, partial reflection, non - reflection, and nonconformity. The results of the analysis showed that the functional aspect was the highest with 68.3%, the material aspect (53%), the landscape aspect (22.3%), the productive aspect (14.7%) and the morphological aspect (12.2%), and maintenance / management (10.6%). In addition, the facilities with the lowest fitness in each aspect are bicycle shelter in landscape aspect, bicycle storage box and trash can in form aspect, shower room in material aspect, trash can in functional aspect, showroom, guide maps and drinking fountain in product aspect, showroom In maintenance aspect. In order to improve the sustainability of coastal facilities in the future, it is necessary to complement the administrative and landscape aspects. In coastal facilities, it is necessary to consider the sustainability planning index, especially for showers, taking into account the specificity of beaches. Consideration should be given to various aspects of sustainability for bike shelters and trash facilities. Through this study, we have proposed the plan elements to systematize, supplement, and improve the planning index for sustainability improvement in coastal facilities planning.

철결핍성 빈혈을 가진 영유아에서 영양학적 평가 및 영양상담 효과

김자경,고은영,이유진,전용훈,김순기,Kim, Ja Kyoung,Ko, Eun Young,Lee, Yu Jin,Jun, Yong Hun,Kim, Soon Ki 대한소아청소년과학회 2003 Clinical and Experimental Pediatrics (CEP) Vol.46 No.1

목 적 : 영양 상담을 통하여 IDA 환아의 식이력을 평가하고 상담에 대한 보호자의 만족도와 순응도를 평가하기 위해 이 연구를 시행하였다. 방 법 : 1997년부터 2001년 8월까지 IDA로 진단받은 120명의 6-36개월 영유아를 대상으로 하였으며, 부모를 대상으로 수유방법 및 이유방법에 대하여 설문조사와 영양상담을 시행하여 다음과 같은 결과를 얻었다. 결 과 : 1) IDA로 진단받은 120명은 호흡기 감염으로 병원에 내원하거나 입원해서 발견된 경우가 47례(39.1%)로 가장 많았으며, 창백이나 빈혈 증상으로 평가를 위해 내원한 경우는 27례(22.5%)였다. 2) 총 120명 중 82명의 보호자들이 영양상담을 받았으며, 그중 56명(68.3%)이 이유식을 하고 있었다. 주요 이유식으로는 쌀죽이나 미음이 30례(53.6%)로 가장 많았으며, 철분강화 이유식이 9례(16.1%), 달걀이나 고기, 생선 등 철분이 풍부한 음식의 경우는 3례(5.4%)였다. 3) 영양상담을 받은 환아들의 문제점으로는 단계적인 이유를 시행하지 않고 우유병을 12개월 이상 사용하는 경우가 40례(48.8%)였고, 철분강화 이유식을 시행하지 않고 모유 수유만을 하는 경우는 26례(31.7%)였다. 4) 영양상담을 시행한 후 만족도는 87.8%로 높았으며, 치료에 대한 순응도는 영양상담을 시행한 군에서 철분제제만으로 치료한 군보다 유의하게 높았다(85.4% vs 72%). 결 론 : IDA를 갖는 환아들의 공통적인 식이력은 주 영양 공급원이 탄수화물인 경우로 다섯 식품군이 골고루 섭취되지 않을때, 12개월 이상이 되어도 고형식의 섭취는 거의 없으면서 액상식품을 우유병으로 먹이고 있을 때, 과자 등의 스낵이나 쥬스등의 섭취, 6개월 이후 철분강화 이유식을 시행하지 않고 모유 수유만을 하는 경우, 알레르기 등의 질환으로 임의적인 음식의 제한을 하는 경우, 12개월 전에 생우유를 먹이거나 하루에 700cc 이상 먹인 경우 6가지로 정리해 볼 수 있었다. 그리고 전문적인 영양평가 및 IDA 치료의 순응도를 높이기 위해서 영양상담의 필요하다고 사료된다. Purpose : Iron deficiency is still the most common nutrient deficient disorder despite the improvement in general health and nutrition. This study is designed to evaluate the dietary history of infants and young children with iron deficiency anemia(IDA) and the effects of nutritional counseling. Methods : This study was conducted on 120 children from 6 to 36 months of age with IDA. Their parents completed a questionnaire and took counsel for nutrition. IDA was defined as Hb <11.0 g/dL, ferritin <10 ng.mL or transferrin saturation <15%, or Hb increase >1 g/dL after iron preparation. The questionnaire consisted of their feeding patterns, weaning time and kinds of food. Results : In the 120 infants and young children aged from 6 to 36 months, the parents of 82 cases was counseled about nutrition. Fifty six infants among 82 cases have started weaning and the main foods of weaning were rice and/or rice gruel. Nutritional problems in weaning were that some children over one year of age were using a bottle, and parents restricted weaning food at will because of allergic disease or chronic disease. Most parents were satisfied with the nutritional counseling given from a clinical dietitian and showed good compliance. Conclusion : Many infants and young children with IDA were provided with non iron-fortified foods and made an inadequate wean. Most parents were satisfied with the nutritional counseling and showed good compliance. The need of dietary counseling was required for prevention and treatment of iron deficiency anemia because of inadequate weaning.

리사이클 디자인 제품의 브랜드 활성화 전략

김자경,Kim, Ja-Gyeong (사)한국포장협회 2014 包裝界 Vol.249 No.-

청각장애 중학생과 일반 중학생의 불안, 우울, 그리고 학교적응 간의 관계

김자경 ( Ja Kyoung Kim ),김주영 ( Ju Young Kim ),김남진 ( Nam Jin Kim ) 한국특수아동학회 2007 특수아동교육연구 Vol.9 No.4

CRA 전략 기반 수감각 프로그램의 효과 검증: 중재반응모델 2단계 적용

김자경(Kim, Jakyoung),강혜진(Kang, Hyejin),서주영(Seo, Juyoung),신정원(Shin, Jeongwon) 부산대학교 교육발전연구소 2019 교육혁신연구 Vol.29 No.4

연구목적: 본 연구는 CRA 전략 기반 수감각 2단계 중재가 수학장애 위험군 아동의 수감각과 수학성취도 향상에 효과적인지 검증하는 데 목적이 있다. 연구방법: 수감각 수준이 낮은(-1SD 이하) 만 6세 아동 5명을 대상으로 수감각 2단계 중재를 실시한 후 수감각과 수학성취도 검사에서 향상이 있는지 알아보았다. 수감각 2단계 중재는 매 차시 C(구체적)-R(표상적)-A(추상적) 단계의 활동으로 5주간 총 29회기 진행되었다. 각 회기는 도입(5분), 전개(20분), 정리(5분)로 구성되었다. 수감각의 진전도를 확인하기 위해, 김자경 등(2018)이 개발한 수감각 검사로 사전, 중간, 사후 검사를 실시하였으며, 수학성취도 향상을 확인하기 위해 KISE-BATT:수 영역 검사로 사전, 사후검사를 실시하였다. 연구결과: 첫째, 수학장애 위험군 아동들의 수감각 총점에 대한 진전도를 분석해 보면, 매회기 점차적으로 향상되는 경향을 나타냈다. 수감각 사전-사후 점수의 비교를 위해 비모수통계를 실시한 결과, 통계적으로 유의한 변화를 보였다. 둘째, 수학장애 위험군 아동들의 수학성취도 사전-사후 점수의 비교를 위해 비모수통계를 실시한 결과, 통계적으로 유의한 변화가 나타나지 않았다. 하지만 한 명을 제외한 모든 아동의 수학성취도 사후 점수가 사전 점수보다 향상되었다. 논의 및 결론: 본 연구를 통해 수감각 2단계 중재는 수학장애 위험군 아동의 수감각 향상에 효과가 있음을 알 수 있다. Purpose: The purpose of this study was to examine the effectiveness of the Number Sense Teaching Program based on CRA (concrete-representational-abstract) for children at risk for mathematics learning disabilities. Method: 5 children at risk for mathematics learning disabilities (6-year-old) participated in the CRA-based Number Sense Teaching Program for 29 sessions during 5 weeks. Each session was made of introduction (5 min), main lesson (20 min), and wrap-up (5 min). The main lesson consisted of C(Concrete)-R (Representational)-A (Abstract) stages. Children at risk for mathematics learning disabilities were measured with a Number Sense Test, developed by Kim et al. (2018) and the Number Subtest of KISE-BATT: Math (Basic Academic Achievement Test: Math), which is a standardized test of math achievement. Results: The results from this study were as following: First, the number sense of children at risk for mathematics learning disabilities gradually improved during the intervention. The non-parametric test was performed to compare the pre- and post-test scores of the number sense, and statistically significant changes were observed. Second, the non-parametric test was performed to compare the pre- and post-test scores of the math achievement in Number, and statistically significant changes were not observed. However, all children except one showed higher scores on the post-test than the pre-test on the Number Subtest of KISE-BAAT: Math. Conclusion: The results of this study showed that the number sense intervention based on CRA was effective in improving the number sense of the children at risk for mathematics learning disabilities.

빈뇨와 복통, 설사로 발현된 방광과 위장관을 동시 침범한 과호산구증가증후군 1예

김자경 ( Ja Kyung Kim ),김주희 ( Joo Hee Kim ),박한민 ( Han Min Park ),정용설 ( Yong Seol Jeong ),최청조 ( Chung Jo Choi ),나성균 ( Seong Kyun Na ),김종혁 ( Jong Hyeok Kim ),송영림 ( Young Rim Song ),황용일 ( Yong Il Hwang ),장승 대한천식알레르기학회 2015 Allergy Asthma & Respiratory Disease Vol.3 No.1

Idiopathic hypereosinophilic syndrome (IHES) is a rare disorder defined by persistent blood eosinophilia, evidence of eosinophil-associated organ dysfunction and absence of secondary causes. Eosinophilic infiltration and its mediator release can cause damage to multiple organs. Although IHES can involve every organ system, bladder involvement is rarely evidenced. We recently reported a case of IHES with both bladder and gastrointestinal tract involvement. A 43-year-old woman visited Hallym University Sacred Heart Hospital complaining of urinary frequency, abdominal pain, and diarrhea for several months. Abdominal pelvic computed tomographic scan showed diffuse wall thickenings in her bladder and colon with small pelvic ascites. Laboratory investigation showed a marked peripheral eosinophilia and tissue biopsies confirmed eosinophilic infiltration in the bladder wall, esophagus, and duodenum. The patient was treated with prednisolone and her eosinophilia and symptoms have gradually improved.

기상 변화에 따른 알레르기 유발식물과 알레르기질환 간의 상관관계

김주화 ( Joo Hwa Kim ),오재원 ( Jae Won Oh ),이하백 ( Ha Baik Lee ),김성원 ( Seong Won Kim ),정혜리 ( Hai Lee Chung ),국명희 ( Myung Hee Kook ),박강서 ( Kang Seo Park ),김봉성 ( Bong Seong Kim ),김자경 ( Ja Kyung Kim ),이동진 ( Do 대한천식알레르기학회 2014 Allergy Asthma & Respiratory Disease Vol.2 No.1

Purpose: There are a number of reports suggesting that widespread propagation of weeds and high concentration of weed pollen have been contributed to climate change. We investigated the inte rrelationship between allergenic pollen concentration, allergic symptom and meteorological factor. Methods: We collected data of pollen concentration and meteorological factors in 7 stations nationwide during between 1998 and 2012. We recruited total 297 allergic patients sensitized to weed pollens from each station, conducted a survey about allergic symptom, and calculated symptom index. We surveyed the vegetation area of ragweed and Japanese hop. Based on these data, we performed the long-term trend analysis (X11-ARIMA, autoregressive integrated moving average) on regional pollen concentration, and correlation analysis to investigate the interrelation between weed pollen concentration, allery symptom index and meteorological factor. We have also done regression analysis on vegetation area and maximal pollen concentration. Results: Long-term trend analysis showed the increasing trend of pllen concentration in Seoul. Weed pollen concentration, allergy symptom index and each meteorological factor were not correlated significantly. Regression analysis revealed that increase of weed vegetation area results in increase of weed pollen concentration. Through this regression equation, we estimated the vegetation area that can product pollen concentration triggering allergenic risk. Conclusion: Meteorological factors, pollen concentration and allergic symptoms should be consistently assessed and the relationship between each factor should be analyzed, considering climate change. It is necessary to verify the equation for pollen estimation by vegetation area and set up a policy for vegetation control focused on the reduction of allergenic pollen. (Allergy Asthma Respir Dis 2014;2:48-58)

기상 변화에 따른 알레르기 유발식물과 알레르기질환 간의 상관관계

김주화 ( Joo Hwa Kim ),오재원 ( Jae Won Oh ),이하백 ( Ha Baik Lee ),김성원 ( Seong Won Kim ),정혜리 ( Hai Lee Chung ),국명희 ( Myung Hee Kook ),박강서 ( Kang Seo Park ),김봉성 ( Bong Seong Kim ),김자경 ( Ja Kyung Kim ),이동진 ( Do 대한천식알레르기학회 2015 Allergy Asthma & Respiratory Disease Vol.3 No.3

신문 활용 탐구공동체 교육활동을 통한 일반 중학생의 장애인에 대한 태도 변화 연구

김순자 ( Soon Ja Kim ),김자경 ( Ja Kyoung Kim ),김지훈 ( Ji Hoon Kim ),김기주 ( Ki Ju Kim ) 한국특수아동학회 2007 특수아동교육연구 Vol.9 No.1

본 연구는 비장애학생의 장애인에 대한 태도 변화를 목적으로 실시한 신문 활용 탐구공동체 교육활동에 관한 것이다. 신문 활용 탐구공동체 교육활동은 학생들의 학습 동기 유발과 협동심을 고양시킬 수 있도록 모둠을 편성하여, 사전에 제시된 주제를 중심으로 신문이나 인터넷 신문을 검색하여 과제를 협동하여 해결하게 하는 것으로, 본 연구에서는 78명의 비장애 중학생에게 이 활동을 실시하여 사전, 사후 개방형 질문지를 통해 태도의 변화를 분석하였다. 개방형 질문에는 장애의 의미와 개념, 장애의 유형과 특성, 장애인의 소외된 권리, 장애인을 만났을 때의 느낌, 장애학생과의 조별활동 및 구체적 활동 시의 감정, 장애인에 대한 편견, 장애인이 도움을 요청할 때의 행동, 장애인을 위한 봉사 활동, 장애인에 대한 예절 등이 포함되었으며 학생들의 답변을 유목화하여 분석하였다. 분석 결과, 신문 활용 탐구공동체 교육활동을 통한 장애이해교육은 비장애중학생의 장애인에 대한 태도를 인지적 측면, 정서적 측면, 행동적 측면에서 모두 향상시키는 것으로 나타났다. The purpose of this study is to investigate the effects of the activities of NIE Inquiry Community on changing attitudes of middle school students toward people with disabilities. A total of 78 first-grade students in D middle school of P City were sampled for this study. The attitudes of students without disabilities toward people with disabilities was evaluated with the open-ended questionnaire that consists of 9 items related to cognitive, emotional and behavioral elements. The results indicate that the cognitive, emotional and behavioral attitudes of students without disabilities toward people with disabilities are improved after providing the activities of the NIE inquiry community. Therefore, the result of this study suggests that the activities of the NIE inquiry community is an effective method which helps middle school students without disabilities change their attitudes toward people with disabilities.