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폐동맥 혈전색전증과 혈관염으로 오진된 주변부 폐동맥에서 발생한 폐동맥 내막육종: 증례 보고
Min Seong Kim,Jin Hee Lee,Jung Hee Hong,Il Seon Hwang 대한영상의학회 2023 대한영상의학회지 Vol.84 No.6
Pulmonary artery sarcomas are rare, high-grade malignancies, primarily affecting the proximal elastic pulmonary artery and usually manifesting as tumoral impaction on imaging. Due to similar clinical and imaging findings, pulmonary artery sarcomas are frequently misdiagnosed as pulmonary thromboembolism or, occasionally, as vasculitis. Herein, we reported a case of pulmonary artery intimal sarcoma initially misdiagnosed as pulmonary thromboembolism and vasculitis due to its relatively atypical location and morphology, along with a literature review.
강세나,조명현,현혜선,김지현,고재성,강희경,정해일,김우선,문경철,하일수 대한의학회 2019 Journal of Korean medical science Vol.34 No.24
D-penicillamine has been reported to cause antineutrophil cytoplasmic antibody (ANCA)- associated vasculitis presenting as rapidly progressive glomerulonephritis or pulmonary- renal syndrome mostly in adults. We report a pediatric case of D-penicillamine induced ANCA-associated vasculitis that manifests as a pulmonary-renal syndrome with a mild renal manifestation. A 13-year-old girl who has been taking D-penicillamine for five years under the diagnosis of Wilson disease visited the emergency room because of hemoptysis and dyspnea. She had diffuse pulmonary hemorrhage, microscopic hematuria, and proteinuria. Myeloperoxidase ANCA was positive, and a renal biopsy revealed pauci-immune crescentic glomerulonephritis. Under the diagnosis of D-penicillamine-induced ANCA-associated vasculitis, D-penicillamine was switched to trientine, and the patient was treated with plasmapheresis, glucocorticoid, cyclophosphamide, and mycophenolate mofetil. Pulmonary hemorrhage improved rapidly followed by the disappearance of the hematuria and proteinuria five months later.
Kim, Joo-Hee,Moon, Jun-Il,Kim, Jeong Eun,Choi, Gil-Soon,Park, Hae-Sim,Ye, Young-Min,Yim, Hyunee The Korean Academy of Asthma, Allergy and Clinical 2010 Allergy, Asthma & Immunology Research Vol.2 No.1
<P>Anti-tuberculosis drugs frequently result in cutaneous adverse reactions, including pruritus, maculopapular exanthems, and urticaria. However, anti-tuberculosis drug-associated cutaneous leukocytoclastic vasculitis (CLV) has been rarely reported. We describe a case of CLV induced by rifampin and pyrazinamide. A 38-year-old male had been diagnosed with pulmonary tuberculosis two months ago and then he started standard anti-tuberculosis therapy with isoniazid, rifampin, ethambutol, and pyrazinamide. Purpuric lesions developed in the extremities after 1.5 months of anti-tuberculosis medication; the lesions progressively spread over the entire body. Histopathology of the purpuric skin lesion was consistent with leukocytoclastic vasculitis. The skin lesion improved after cessation of anti-tuberculosis medications and treatment with oral corticosteroids and antihistamines. Anti-tuberculosis drugs were rechallenged one at a time over 3 days. Purpura recurred on the right forearm and forehead after taking 300 mg of rifampin. The skin lesion disappeared after taking oral prednisolone. Finally, 1,500 mg of pyrazinamide was readministrated, and then purpuric lesions recurred on both forearms. This report describes a case of leukocytoclastic vasculitis secondary to rifampin and pyrazinamide therapy.</P>
임성용 ( Seong Yong Lim ) 대한결핵 및 호흡기학회 2010 Tuberculosis and Respiratory Diseases Vol.69 No.4
Pulmonary vascular disease is a category of disorders, including pulmonary hypertension, pulmonary embolism or chronic thromboembolic pulmonary hypertension, pulmonary vasculitis, pulmonary vascular disease secondary to chronic respiratory disease, and pulmonary vascular tumor and malformations. This article reviews the recent advances in this wide spectrum of pulmonary vascular diseases.
제갈양진(Yang Jin Jegal),장현규(Hyun Kyu Chang),류대식(Dae Sik Ryu),원경숙(Kyoung Sook Won) 대한내과학회 2000 대한내과학회지 Vol.59 No.5
Behcet's disease is a nonspecific vasculitis characterized by exacerbations and remissions of unpredictictable duration. The commom clinical features in most patients are orogenital ulcers, uveitis and skin lesions-especially erythema nodosum-like lesions or positive pathergy test. Among the systemic manifestations of Behcet's disease, pulmonary involvement is very rare and only a few cases have been documented. The main event of pulmonary involvement is vasculitis forming multilocular aneurysms and thrombosis of the pulmonary artery. The commom pulmonary manifestations are hemoptysis, dyspnea, pleuritic chest pain, cough and fever. The prognosis of pulmonary vasculitis is very poor. A 30-year-old male patient with Behcet's disease presented with fever and dyspnea for 10 days. In the past years, his vision of the left eye was lost due to chorioretinitis. He took right hemicolectomy because of the perforation of colonic ulcer. Also he has been suffered from left hemiparesis due to multiple cerebral infarction. We describe a case with Behcet's disease with pulmonary infarction improved with prednisolone and cyclosporine.(Korean J Med 59:535-539, 2000)
Propylthiouracil로 인한 ANCA 양성 혈관염과 동반된 막성 콩팥병증
류광덕 ( Kwang Duck Ryu ),배민정 ( Min Jung Bae ),백동훈 ( Dong Hoon Baek ),신민지 ( Min Ji Shin ),성은영 ( Eun Young Seong ),송상헌 ( Sang Heon Song ),곽임수 ( Ihm Soo Kwak ) 대한내과학회 2011 대한내과학회지 Vol.81 No.3
Vasculitis is one of the rare complications of antithyroid drugs. In most cases, it is associated with ANCA and usually involves more than one organ. Renal involvement is the most common manifestation, and mainly presents as pauci-immune glomerulonephritis. We experienced MPO-ANCA-positive vasculitis and renal involvement presenting as membranous nephropathy following propylthiouracil (PTU) treatment. Cases of MPO-ANCA-positive vasculitis with membranous nephropathy are very uncommon, and the relationship between PTU and glomerulonephritis with immune complex deposition is unclear at present. A 58-year-old woman who had been treated with PTU for Graves` disease was admitted because of dyspnea and general edema. Chest computed tomography showed multiple nodules in both lung fields. The serum level of MPO-ANCA was positive. Initial laboratory findings included proteinuria, hematuria and increased serum creatinine. We thought that MPO-ANCA-associated vasculitis was induced by PTU and renal involvement. Renal biopsy revealed membranous nephropathy. (Korean J Med 2011;81:397-402)
손창우,조정환,송인욱,박정은,신경철,정진홍,이관호 영남대학교 의과대학 2009 Yeungnam University Journal of Medicine Vol.26 No.2
Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis that typically affects the medium-sized muscular arteries, with occasional involvement of the small muscular arteries. As with other vasculitides, PAN can affect any organ system, including the cardiovascular, gastrointestinal and central nervous systems. The prognosis for patients with untreated PAN is relatively poor, with five-year survival rates of approximately 13 percent. The outcome has improved with proper therapy to approximately 80 percent survival at five years. We report here on a case of a 46 year old man with polyarteritis nodosa and who suffered from pulmonary tuberculosis.
Propylthiouracil로 유발된 미만성 폐출혈: 임상 및 방사선학적 소견
조영준,김정숙,김지영,최수전 대한영상의학회 2007 대한영상의학회지 Vol.56 No.5
Propylthiouracil (PTU) is a drug that's used to manage hyperthyroidism and it can, on rare occasions, induce antineutrophil cytoplasmic antibody-associated vasculitis that involves multiple organ systems and it can also cause extremely rare isolated or diffuse pulmonary hemorrhage. We report here on a case of a patient who developed diffuse pulmonary hemorrhage after she had been taking PTU for five years. The patient is a 33-yearold woman who presented with hemoptysis. Simple chest radiographs and the chest CT showed bilateral ground-glass opacity, consolidation and pulmonary arterial hypertension. The bronchoalveolar lavage fluid revealed alveolar hemorrhage. The laboratory values showed increased perinuclear-antineutrophil cytoplasmic antibody (p-ANCA) and anti-peroxidase antibody titers. Propylthiouracil은 갑상선 기능 항진증의 치료약물로써 드물게 면역학적 반응에 의한 혈관염으로 폐출혈을 포함하여 여러 장기에 부작용을 가져올 수 있다. 저자들은 5년 동안 갑상선 항진증으로 propylthiouracil 을 복용해온 36세의 여자환자가 객혈과 더불어 전산화단층촬영에서 폐동맥 고혈압과 미만성 간유리 음영을 보였고, 기관지 세척(BAL)에서 폐출혈 소견이 있었으며 혈청학적 검사에서 perinuclear-antineutrophil cytoplasmic antibody(p-ANCA)와 antiperoxidase antibody 양성을 보여 propylthiouracil 복용으로 유발된 미만성 폐포 출혈로 진단된 증례를 경험하였기에 문헌고찰과 함께 보고하고자 한다.
Pulmonary Artery Thrombosis Associated with Scrub Typhus
조정환,이찬희 대한감염학회 2019 Infection and Chemotherapy Vol.51 No.1
Scrub typhus is an acute febrile disease caused by Orientia tsutsugamushi, and the clinical course varies from mild and self-limiting to fatal. We describe a rare case of a pulmonary artery thrombosis associated with scrub typhus. Vasculitis via endothelial dysfunction caused by scrub typhus could be considered as the main mechanism.