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Isolated Right Ventricular Apical Hypoplasia: A Case Report with 18 Years of Follow Up
Oya Takashi,Kitagawa Kakuya,Kokawa Takanori,Nakajima Hiroshi,Nakamori Shiro,Ogihara Yoshito,Nakata Kei,Ishida Masaki,Ichikawa Yasutaka,Sakuma Hajime 아시아심장혈관영상의학회 2021 Cardiovascular Imaging Asia Vol.5 No.2
Isolated right ventricular (RV) hypoplasia is a rare congenital anomaly in which the apical trabecular component of the ventricle fails to develop. In severe forms of isolated RV hypoplasia, patients usually develop cyanosis early in life and require prompt surgical intervention. Mild forms, however, can be asymptomatic until the development of severe tricuspid regurgitation due to annular dilatation. We report a 50-year-old woman with isolated RV apical hypoplasia who presented to our hospital 18 years ago and was followed with serial imaging studies.