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원발성 피부 CD30 음성 대형 T 세포 림프종 1 예
천은영(Eun Young Chun),황성원(Sung Won Whang),김유찬(You Chan Kim),김수찬(Soo Chan Kim) 대한피부과학회 2002 대한피부과학회지 Vol.40 No.8
Primary cutaneous CD30-negative large T-cell lymphoma without prior concurrent mycosis fungoides represents a distinct group of cutaneous T-cell lymphoma with an aggressive clinical behavior. Primary cutaneous CD30-negative large T-cell lymphoma is a rare disorder which represents only about 5% of primary cutaneous T-cell lymphoma. A 51-year-old woman presented with a rapid growing, ulcerative plaque on the right lower leg of 2 years duration. Histologically, it showed diffuse infiltrates with a predominance of medium-sized to large pleomorphic lymphocytes in the dermis and subcutaneous fat layers, which stained positively with CD3 and negatively with CD20, CD30, CD56 on immunohistochemical staining. There was no evidence of extracutaneous metastsis.
임하성 ( Ha Seong Lim ),황성원 ( Sung Won Whang ),윤도흠 ( Do Heum Yoon ),이민걸 ( Min Geol Lee ) 대한피부과학회 2001 대한피부과학회지 Vol.39 No.9
Unilateral localized hyperhidrosis over scalp and face is an extremely rare disease that usually has undetermined origin. We report a case of idiopathic unilateral localized hyperhidrosis over left scalp and face. A 55-year-old female patient with unilateral hyperhidrosis that is localized in the left side of scalp and face visited our dermatology clinic. She had increased sweating in left face and scalp, securring in summer for 3 years. She complained of the exacerbation by thermal and gustatory stimuli and exercise. The starch iodine test and digital infrared thermal imaging test revealed a marked increase in sweat gland activity on the affected areas as compared to the contralateral normal sites.
한국인의 부분 백피증(Piebaldism) 1에 대한 임상적 고찰
한승경(Seung Kyung Hann),황성원(Sung Won Whang),김수민(Soo Min Kim) 대한피부과학회 2000 대한피부과학회지 Vol.38 No.6
Background:Piebaldism is an uncommon congenital disease inherited in autosomal dominant pattern. It is characterized by stable leukoderma with white forelock and vitiligo-like amelanotic macules usually containing a few normally pigmented or hyperpigmented macules. There have been a few case reports, but no clinical study in Koreans. Objective:The purpose of this study was to investigate characteristic clinical features in Korean patients with piebaldism different from that of Caucasian. Methods:We evaluated 11 patients with piebaldism using retrospective method and telephone survey in regard to sex, family history, clinical features such as distribution of hypopigmented patches, white forelock, normo- or hyperpismented macules within hypopigmented patches, hyperpigmented macules in normal skin, associated systemic disease, and effect of treatment. Results:Ten patients showed autosomal dominant features but one occurred sporadically. The ratio of male to female was 3:8, and only 6 patients had white forelock. The most common site of hypopigmented patches was the lower leg(in all patients), followed by abdomen, left foot and left buttock, and chest. All patients had normo- or hyperpismented macules in hypopigmented patches, and 4 had hyperpigmented lesion in normal skin. Down's syndrome was associated in one case. We treated 3 cases with epidermal graft. Conclusion:Most cases were consistent with other western reports. But our patients revealed female predominance(3:8), lower incidence of white forelock(about 55%), frequent lower leg involvement(100%), and uncommon distribution of skin lesion such as foot and buttock. These differences reflected characteristic clinical features of piebaldism in Koreans different from those of Caucasians. (Korean J Dermatol 2000;38(6):721~728)
이광훈,황성원 대한피부과학회 2000 大韓皮膚科學會誌 Vol.38 No.10
Generalized eruptive histiocytoma is a papular, nonlipidic, self-healing histiocytosis affecting mainly adults. Clinically the disease is characterized by an asymptomatic, widespread, frequently symmetrical eruption of numerous dark red or bluish red papules. In adults the lesions are symmetrically distributed and may involve mucous membranes, while in children the lesions are irregularly scattered over the entire body and mucous membranes spare. We herein report a case of generalized eruptive histiocytoma developed in a 3-year-old boy. He was seen with brownish, flat papules on the face, trunk and both proximal portions of extremities. Histological and immunohistochemical investigation revealed monomorphous infiltration of S-100, CD1a negative, lysozyme positive histiocytes in the upper dermis. Neither cells with foamy cytoplasm nor giant cells was found. He did not show any disease progression without treatment, so now in regular follow-up for exaggeration.
이상주,한승경,황성원,정한길 대한피부과학회 1999 大韓皮膚科學會誌 Vol.37 No.11
Linear focal elastosis was first described by Burket et al. in 1989 in three elderly men with palpable striae-like yellow bands on their backs. Microscopic examination revealed many fine wavy bundles of elastic fibers separating the collagen in the mid to reticular dermis. The patients' ages range a from 17 to 87 years but this disease seems to be more common in younger age; men are more commonly affected. The cause of this disease has been suggested to be hereditary predisposition, unusual form of striae distensae or keloidal repair of striae distensae. We report linear focal elatosis with typical clinical and pathological features in a 15-year-old boy.
김동수,이광훈,황성원 대한피부과학회 2000 大韓皮膚科學會誌 Vol.38 No.12
Early-onset childhood sarcoidosis is a unique form of the disease characterized by the triad of rash, uveitis, and arthritis in patients presenting before age 4 years. We report a case of early onset childhood sarcoidosis in a 4-year-old girl. She presented with fever, right ankle joint swelling, multiple skin lesions on whole body and was diagnosed as juvenile rheumatoid arthritis in Department of Pediatrics. She was transferred to Department of Dermatology for skin evaluation, histological investigation revealed well-circumscribed, non-caseating naked granuloma with epitheloid cells, histiocytes, lymphocytes on the upper dermis. Laboratory evaluation, chest X-ray, and ophthalmologic evaluation were all within normal limits. She was treated with systemic steroid, methotrexate, non-steroidal anti-inflammatory drugs and follow up evaluation will be planned for possible eye involvement.
이민걸,이종두,강진문,황성원 대한피부과학회 2000 大韓皮膚科學會誌 Vol.38 No.3
The term cutaneous chylous reflux refers to the back flow of chyle from its normal route and the discharge of chyle from the skin. Primary chylous reflux suggests the absence of an apparent etiology and may be due to malformations of mesenteric lymphatics. On the other hand, secondary chylous reflux is the result from irradiation, neoplasm, trauma and infection with filariasis. Here we report a case of primary cutaneous chylous reflux that has a unique clinical feature.
성별·연령에 따른 여성복의 디자인 선호도 조사 : 정숙성을 중심으로
양희경,김연호,박상희,반정민,이준미,한경희,황성원 연세대학교 생활과학대학 1990 婦學 Vol.23 No.-
1. 정숙성에 대한 태도는 집단별로 유의적인 차이를 보였다. 2. 의복디자인 선호도는 집단별로 유의적인 차이를 보였다. 3. 남자는 연령에 관계없이 모두 일반적으로 선호하는 디자인보다 자신의 딸·애인을 위한 옷으로 보다 보수적인 디자인을 선호하였다. 50대 여성은 일반적인 선호와 자신의 딸을 위한 선호와 차이가 적었다.