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안검황색종의 임상병리학적 연구; 고지혈증과 심혈관계 질환에 대한 임상적 지표로서의 의의
지민선 ( Min Sun Jee ),장성은 ( Sung Eun Chang ),최지호 ( Jee Ho Choi ),성경제 ( Kyung Jeh Sung ),문기찬 ( Kee Chan Moon ),고재경 ( Jai Kyoung Koh ) 대한피부과학회 2003 대한피부과학회지 Vol.41 No.3
Background:Xanthelasma palpebrarum is the most common cutaneous xanthoma. Although xanthelasma is a type of xanthoma, a half of most serious patients are known to be normolipemic. Objective:This study is an attempt to elucidate the clinical and pathologic
피부 비만세포증 30 예의 임상 및 병리 조직학적 고찰
장성은(Sung Eun Chang),강숙경(Sook Kyoung Kang),지민선(Min Sun Jee),최지호(Jee Ho Choi),성경제(Kyung Jeh Sung),문기찬(Kee Chan Moon),고재경(Jai Kyoung Koh) 대한피부과학회 2002 대한피부과학회지 Vol.40 No.5
N/A Background : Mastoeytosis is characterized by accumulation of mast cells in various organs, most frequently in skin. Cutaneous mastoeytosis is a relatively rare disease in outpatient clinics and the clinicopathological study has not been done yet in Korea. Objective : The ain of this study is to analyse the clinieopathological features of cutaneous mastocytosis. In addition, we examined CDU7 expression in the skin biopsy specimens immunohistochemically Methods : Thirty cases of cutaneous mastocytosis were collected from 1990 to 1999 in Asan Medical Center. Clinical records, photographs. and biopsy slides were reviewed. In each biopsy specimen, CDU7 was stained by immunoperoxidase method. Results : Among 30 cases, 29 cases were childhood type urticaria pigmeniosa(76.7 %) or mastocytoma(20.2%) and only I case occurred after 16 years of age. The incidence showed a peak under 1 year old (70.0%) and mates affected 2.3 times as much as females. The trunk and distal extremities are the most common site of urticaria pigmentosa and mastocytoma respectively. CD117 was strongly positive in all cases of utricaria pigmentosa (both child and adult type) and mastocytoma. Conclusion : Urticaria pigmentosa of infantile onset was the most common, followed by infantile mastocytoma. Systemic reactive manifestations are rate in cutaneous mastocytosis. The strong expression of CD117 was seen regardless of cutancous mastocytoses.
중독성 표피 괴사융해증에서 고용량 면역 글로불린 정맥주사의 치료효과에 대한 고찰
김경진(Kyoung Jin Kim),지민선(Min Sun Jee),한만회(Man Heui Han),최지호(Jee Ho Choi),성경제(Kyung Jeh Sung),문기찬(Kee Chan Moon),고재경(Jai Kyoung Koh) 대한피부과학회 2002 대한피부과학회지 Vol.40 No.7
N/A Background : Toxic epidermal necrolysis(TEN) is the most dramatic and life-threatening cutaneous drug reaction. However, specific and effective treatment for TEN have not yet been identified. Recently several reports suggested that high dose intravenous immunoglobulin(Ⅳ Ig) treatment has produced good results in patients with TEN. Objective : To analyze the efficacy and side effects of Ⅳ Ig in treatement of TEN. Methods : Ten patients with clinicopathological diagnosis of TEN were treated with IV Ig(1.6-3.4g/㎏), and clinical efficacy and side effects were observed. Results : Nine patients were healed and one died of sepsis. Interruption of further epidermal detachment occurred after an average 3 days from the onset of Ⅳ Ig therapy. Complete wound healing occurred after an average of 14.3 days. The side effects of Ⅳ Ig including headache, myalgia, nausea, transient neutropenia, and coombs positive hemolytic anemia were observed in 4 patients but normalized after cessation of Ⅳ Ig therapy. Three of them showed complete healing of detached skin but died with aggravation of underlying disease. Conclusion : Ⅳ Ig therapy represents a safe and very effective treatment for TEN. Furthermore, intensive care for underlying diseases is also very important for reducing the mortality rate in patients with TEN.
서호석 ( Ho Seok Suh ),지민선 ( Min Sun Jee ),김형훈 ( Hyung Hun Kim ),최지호 ( Jee Ho Choi ),성경제 ( Kyung Jeh Sung ),문기찬 ( Kee Chan Moon ),고재경 ( Jai Kyoung Koh ) 대한피부과학회 2003 대한피부과학회지 Vol.41 No.1
Cutaneous larva migrans(CLM) is a creeping cutaneous eruption that results from skin invasion by the larval form of nematodes. We experienced two patients who had typical clinical findings of CLM. One patient had a history of contact with possibly contami
지민선,서호석,최지호,성경제,문기찬,고재경 대한피부과학회 2002 大韓皮膚科學會誌 Vol.40 No.7
Mondor's disease is an uncommon superficial thrombophlebitis, usually of thracoabdominal wall. The exact cause is unclear, but it is suggested that the trauma, strenous exercise, breast surgery are often associated. Clinically, it is characterized by a palpable, tender, linear cutaneous groove and it is always almost unilateral. We report a case of bilateral Mondor's disease. 49 year old female presented a cord like subcutaneous lesion on right thoracoabdomial wall. She had a history of strenous exercise for several weeks. Histologic exam reveals thrombophlebitis. A week later, the patient had another same linear subcutaeous lesion on left abdomen.
지민선,김형훈,장성은,최지호,성경제,문기찬,고재경 대한피부과학회 2002 大韓皮膚科學會誌 Vol.40 No.11
Lichen sclerosus et atrophicus is a benign, chronic inflammatory dermatosis with multifactorial origin. It is most common in the vulvar and perianal areas, but it may involve any other area, rarely face, oral mucosa, and palm and sole. Especially, lichen sclerosus et atrophicus on face is more difficult in diagnosis due to atypical location and may be confused with morphea, discoid lupus erythematosus, vitiligo, and atophic scar. We, herein, present a case of facial lichen sclerosus et atrophicus with central brownish atrophic change in a 21-year-old man. The lesion showed atypical clinical feature and unusual location. But histologic examination revealed typical features of lichen sclerosus et atrophicus.
지민선,김형훈,이미우,최지호,성경제,문기찬,고재경 대한피부과학회 2002 대한피부과학회지 Vol.40 No.12
Clear cell sarcoma is a rare malignant soft tissue neoplasm with unknown oringin. It is slow growing tumor, but uncommonly, it shows rapidly progressive course. In Korea, there has been rare case of clear cell sarcoma especially with systemic metastasis, We herein present a case of clear cell sarcoma rapidly progressing with systemic metastasis. She had a deep seated nodule on left heel and inguinal and abdominal lymphadenopathy at the initial presentation. While chemotherapy, acute renal failure occurred and it was suspicious from abdominal ultrasono that both kidneys were invaded with clear cell sarcoma. She died with repiratory failure. (Korean J Dermatol 2002;40(12) : 1591∼1593)
지민선,이득표,장성은,최지호,성경제,문기찬,고재경 대한피부과학회 2003 大韓皮膚科學會誌 Vol.41 No.3
Acquired fibrokeratoma is a rare, benign tumor which occurs most frequently on the fingers. Because of the digital predilection, a term of digital fibrokeratoma has been frequently used. We present here two cases of acquired fibrokeratoma occurring on the prepatellar area and the proximal nail bed which are unusual sites of this lesion. A skin-colored, hyperkeratotic tumor with finger-like projection was found on the prepatellar area of a 29-year-old man and a round pedunculated nodule was found on the proximal nail bed of the second finger of a 74-year-old woman. Histopathologic examination revealed typical features of acquired fibrokeratoma. (Korean J Dermatol 2003;41(3) : 403∼405)
김경진,문기찬,성경제,최지호,고재경,지민선 대한피부과학회 2001 대한피부과학회지 Vol.39 No.11
Tinea incognito has been used to describe a dermatophyte infection modified by topical or systemic corticosteroid treatment. Lesions are often atypical appearing and the diagnosis is frequently delayed or missed even though by skilled dermatologists. We present here a 70-year-old female patient who had been treated with topical steroid ointment for the erythematous papules on the face and scalp under the diagnosis of contact dermatitis. Initially the lesions were regarded as a folliculitis, but a potassium hydroxide (KOH) preparation showed many fungal hyphae. A fungal culture grew Trichophyton rubrum.
지민선,최혜진,최지호,성경제,문기찬,고재경 대한피부과학회 2003 大韓皮膚科學會誌 Vol.41 No.4
Mucormycosis is a rare and opportunistic infection usually associated with hematologic diseases, diabetes mellitus, renal failure, solid tumors, and organ transplantations. We present here a considered case of disseminated rnucormycosis in renal transplant recipient. A 60-year-old man who had undergone second kidney transplantation for a month visited emergency room due to 5 day history of cough with spiking fever and abnormal mental status and vital signs were rapidly deteriorated. Septic shock was suspicious. He was admitted to ICU and treated with broad spectrum antibiotics and antiviral agents, but there was no improvement. A few days later, several large hemorrhagic blisters and purpura occurred on the face, trunk and both lower extremities. The histopathologic examination from skin specimen revealed large, broad, nonseptate hyphae branched at right angles in the dermis and blood vessels, which was consistent with mucormycosis. But the skin culture for fungus was negative. He had had no skin trauma history and evidence. So we considered the disseminated mucormycosis from unknown primary origin. He died of progressive respiratory failure before antifungal treatment. (Korean J Dermatol 2003;41(4) : 50l-504)