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히르슈슈프룽병의 One-stage Transanal Endorectal Pull-through 술식에서 대장조영술의 의의
신만식,이미정,김명준,홍영주,장혜경,한석주,오정탁,Shin, Man Sik,Lee, Mi Jung,Kim, Myung Joon,Hong, Young Ju,Chang, He Kyung,Han, Seok Joo,Oh, Jung-Tak 대한소아외과학회 2012 소아외과 Vol.18 No.2
In one-stage transanal endorectal pull-through operation (TERPT) for Hirschsprung disease, preoperative evaluation by contrast enema (CE) is important tool in aspect of planning of surgical procedure as well as diagnosis. This study was to evaluate the significance of CE for identifying the extent of aganglionic bowel. A retrospective analysis was performed in 40 patients who underwent TERPT between 2003 and 2011. The authors reviewed the CE studies and their correlation with pathologic extent of aganglionosis. Total 66 contrast enemas were performed in 40 patients. Twenty patients underwent single CE, but 20 patients required multiple CEs. In single CE group, 17 had clear radiographic transition zone, but 3 had less definite transition zone. In multiple CE group, 17 patients who had equivocal finding in first or second CE had definite radiographic transition zone, but 3 patients of this group had less definite radiographic transition zones. Overall, 34 patients (85%)had clear radiographic transition zone by single or repeated CE. One (2.9%) out of 34 patients with clear radiographic transition zone had discordance between radiographic and pathologic transition zone. In contrast 4 (66.7%) out of 6 patients with equivocal radiographic transition zone had discordance between radiographic and pathologic transition zone. Observation of clear radiographic transition zone is important in preparation of TERPT, and repeated CE is helpful to reduce the discordance between radiographic and pathologic transition zone. Awareness of the possibility of discordance is also important if radiographic transitional zone is not clear.
미숙아에서 장막층의 섬유 끈에 의한 선천적 위 출구 폐쇄 1례
양소민 ( So Min Yang ),은호선 ( Ho Seon Eun ),이순민 ( Soon Min Lee ),장혜경 ( He Kyung Chang ),박국인 ( Kook In Park ),남궁란 ( Gung Ran Nam ) 대한주산의학회 2014 Perinatology Vol.25 No.4
Most of the gastric outlet obstruction symptoms like vomiting and abdominal distension were caused bycongenital anatomical abnormality in a neonate. Abnormal structures associated with congenital gastricoutlet obstruction have been categorized by its site and extent of obstruction. We report one case of persistingvomiting in a premature infant caused by serosal fibrous band in gastric outlet lesion, excluded from thecategory of congenital gastric outlet obstruction.