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좌심실 게실을 동반한 Cantrell씨 증후군으로 진단된 신생아 1례
양혜경 ( Hea Kyoung Yang ),김아영 ( Ah Young Kim ),임령경 ( Ryoung Kyoung Lim ),박경희 ( Kyung Hee Park ),변신연 ( Shin Yun Byun ) 대한주산의학회 2014 Perinatology Vol.25 No.1
Cantrell`s syndrome is a rare congenital anomaly, consists of five malformations. There are the midline abdominal wall defect, the defect of sterna lower part, an agenesis of the anterior part of the diaphragm, an absence of the diaphragmatic pericardium, and the congenital intracardiac problem. We diagnosed Cantrell`s syndrome with left ventricular diverticulum in a female neonate with no perinatal problems. She experienced an one- staged operation and discharged with no complications. We report a case with brief review of the literature.
소아에서 성공한 isoniazid와 rifampin에 대한 신속 탈감작요법 1예
이혜림 ( Heirim Lee ),김민선 ( Min-sun Kim ),양혜경 ( Hea-kyoung Yang ),김민지 ( Minji Kim ),이지영 ( Ji Young Lee ),김종민 ( Jong-min Kim ),강지만 ( Ji-man Kang ),김예진 ( Yae-jean Kim ),안강모 ( Kangmo Ahn ),김지현 ( Jihyun Kim 대한천식알레르기학회 2016 Allergy Asthma & Respiratory Disease Vol.4 No.3
Hypersensitivity reactions to antituberculosis medicine are obstacles to the treatment of tuberculosis. However, rapid drug desensitization can secure successful treatment with essential antituberculosis medicines in pediatric patients. A 17-year-old boy with active pulmonary tuberculosis complained of generalized erythematous rashes, pruritus on the 11th day of tuberculosis treatment. He was diagnosed with hypersensitivity reactions to isoniazid and rifampin by the oral provocation test. After desensitization, the patient continued to take antituberculosis treatment with isoniazid, rifampin, pyrazinamide, and ethambutol. We report here a case of successful desensitization in an adolescent with hypersensitivity to isoniazid and rifampin. (Allergy Asthma Respir Dis 2016;4:212-216)
단일 기관에서 경험한 소아 아토피피부염 환자의 감작 분포
송아리 ( Ari Song ),이지영 ( Ji Young Lee ),양혜경 ( Hea-kyoung Yang ),김민지 ( Minji Kim ),안강모 ( Kangmo Ahn ),이상일 ( Sang-il Lee ),김지현 ( Jihyun Kim ) 대한천식알레르기학회 2016 Allergy Asthma & Respiratory Disease Vol.4 No.4
Purpose: There are few recent data regarding allergic sensitization of atopic dermatitis (AD) in Korea. The aim of this study was to investigate patterns of sensitization according to age and gender in children with AD.Methods: This retrospective study included 4,661 children with AD from 1998 to 2014. The serum specific IgE (sIgE) levels to egg white (EW), cow’s milk (CM), peanut, wheat, soybean, buckwheat, tree nuts, crustaceans, meat, and house dust mites (HDMs) were reviewed. AD was categorized into the extrinsic (ADe) and intrinsic type (ADi) according to the presence or absence of sensitization. The proportion of patients with sIgE to EW or CM greater than the previously reported diagnostic decision point (DDP) was determined.Results: A total of 4,661 children (2,843 boys and 1,818 girls) were collected. We identified 1,857 of 2,663 children (69.7%) with the ADe type and 806 of 2,663 children (30.3%) with the ADi type. The sensitization rates increased with age (P<0.001). EW (59.3%) was the most commonly sensitized food, followed by CM (46.6%), peanut (32.2%), wheat (31.5%), soybean (28.1%), and buckwheat (23.7%). The most commonly sensitized food groups were tree nuts (56.7%) and crustaceans (28.3%). The rate of sensitization to HDMs was 40.1%. In addition, 11.1% and 7.5% of children had levels of sIgE to EW and CM, respectively, higher than the DDP.Conclusion: The incidence of ADe among children with AD was 69.7% and increased with age. The most commonly sensitized food allergen was EW, followed by CM and peanut. (Allergy Asthma Respir Dis 2016:4:290-295)
서혜경 ( Hye Kyung Seo ),김혜영 ( Hye Young Kim ),양혜경 ( Hea Kyoung Yang ),신성현 ( Sung Hyun Shin ),이병기 ( Byung Ki Lee ),김성헌 ( Seong Heon Kim ),김영미 ( Young Mi Kim ) 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 2011 소아알레르기 및 호흡기학회지 Vol.21 No.2
Purpose: Although bronchiolitis obliterans (BO) most often occurs after infection, the incidence of post-transplant BO has recently increased due to the increase of organ and bone marrow transplantation. However, there is limited data on the responses to treatment using measurements of pulmonary function in patients with BO. This study aimed to describe clinical characteristics and pulmonary function in children with BO from a single institute and to compare the responses according to treatment modalities in children with post-infectious BO. Methods: This study was conducted on 22 children who were diagnosed with BO from January 2005 to December 2010. Based on the medical chart, treatment courses and prognosis of the patients were examined retrospectively. The severity of clinical symptoms was determined by the Denver symptom score, basal pulmonary function, and responses to bronchodilators; all parameters were measured and compared between the time of diagnoses and follow-up six months later. Results: The mean age of the patients when diagnosed with BO was 8.3±6.6 years; of those patients, sixteen were boys and six were girls. Nineteen cases of BO were associated with acute infection, and the most common cause of those cases was adenovirus. Three cases of BO occurred following allogeneic bone marrow transplantation for acute myelogenous leukemia. The Denver symptom scores at the time of diagnosis were averaged to 3.95±0.63, and the average symptom score after follow-up of six months was 2.15±0.73. The averages of the % forced vital capacity (FVC), % forced expiratory volume in 1 second (FEV1), and % forced expiratory flow, midexpiratory phase (FEF25-75%) at the time of diagnosis were 69±13%, 40.5±12.7%, and 17.6±7.8%, respectively, and FEV1/FVC was 56.7±10.9%. The averages of %FVC, % FEV1, and %FEF25-75% six months after diagnosis were 78±17.3%, 62.5±16.5%, and 35.6±9.5%, respectively, and FEV1/FVC was improved to 70.7±18.9%. Symptom scores of the group treated with high dose systemic steroids decreased significantly compared to those of the group treated with inhaled corticosteroids (P<0.05). Likewise, improvement of FEV1/FVC after treatment was greater in the group treated with high dose systemic steroids than in the group treated with inhaled corticosteroids (P<0.05). Conclusion: Infections are the more frequent causes of BO in our institute, and adenovirus ismost common. Six-month follow-up study results suggest high dose systemic steroids could lead to better improvement of clinical symptoms and pulmonary function in children with post-infectious BO. [Pediatr Allergy Respir Dis(Korea) 2011;21:123-130]
학부모 및 학교 보건교사의 식품알레르기 인지도 조사: 2015년 전국역학조사
황정윤 ( Jeong Yun Hwang ),김민지 ( Minji Kim ),이지영 ( Ji Young Lee ),양혜경 ( Hea-kyoung Yang ),이기재 ( Kee-jae Lee ),전현영 ( Hyun-young Jeon ),한영신 ( Youngshin Han ),김양희 ( Yang Hee Kim ),김지현 ( Jihyun Kim ),안강모 ( K 대한천식알레르기학회 2018 Allergy Asthma & Respiratory Disease Vol.6 No.2
Purpose: This study aimed to examine the perception of food allergy among parents and school health instructors in Korea. Methods: A nationwide epidemiological survey in Korea was conducted in September 2015. From 17 cities and provinces, a total of 1,000 elementary, middle and high schools were selected by stratified random sampling. Parents and school health instructors were surveyed using a questionnaire on the perception of food allergy. Results: The prevalence of food-induced anaphylaxis was 22.3%. Of 252 children with anaphylaxis, 47.6% were prescribed epinephrine auto-injector (EAI). Forty-three parents (37.7%) were educated about the use of EAI. Parents carrying their own EAI at all times or keeping them at schools were 5.6% and 3.8%, respectively. For the food allergen-labeling system, 42.1% of parents read food labels, and 32.1% were satisfied with the system. Only 35.2% of school health instructors received education on food allergy and anaphylaxis, and 42.5% of them knew how to use EAI. There were 70 children (9.4%) with anaphylaxis in school, and 75.9% of schools had the emergency management system. Conclusion: The awareness of Korean parents and school health instructors on food allergy is still low, and many parents are dissatisfied with the food allergen labeling system. Many school health instructors have difficulty in using EAI in case of anaphylaxis and are insufficiently educated about food allergy. Therefore, it is necessary to establish more systematic food allergy management plans by providing high-quality education to parents and school health instructors and by utilizing legal systems. (Allergy Asthma Respir Dis 2018;6:97-102)
소아의 즉시형 우유와 난백 알레르기의 임상 특성과 식품 노출 형태
이은주 ( Eunjoo Lee ),정경욱 ( Kyunguk Jeong ),이지영 ( Ji Young Lee ),민택기 ( Taek Ki Min ),김민지 ( Minji Kim ),양혜경 ( Hea-kyoung Yang ),이해원 ( Hae Won Lee ),김지현 ( Jihyun Kim ),안강모 ( Kangmo Ahn ),편복양 ( Bok Yang Pyu 대한천식알레르기학회 2017 Allergy Asthma & Respiratory Disease Vol.5 No.6
Purpose: The aim of this study was to evaluate the details of the clinical characteristics and food exposure types at the first symptom onset in immediate-type cow’s milk allergy (CMA) and egg white allergy (EWA) in Korean children. Methods: This study included children with immediate-type CMA (n=288) or EWA (n=233) with symptom onset time of 2 hours or less, who visited Samsung Medical Center, Ajou University Hospital, and Soonchunhyang University Seoul Hospital between September 2014 and August 2015. The details of clinical features and food exposure types at the first symptom onset were evaluated by retrospective medical record review using a standardized case report form. Results: The median ages of first symptom onset were 10 months in CMA and 12 months in EWA. The most common types of exposure at the first symptom in CMA were formula milk (29.5%) and milk (29.5%), followed by cheese (17.7%) and yogurt (14.2%). The most common type of exposure in EWA was boiled eggs (35.6%), followed by rice/porridge/soup containing eggs (27.5%), pan-fried eggs (17.6%), and baked goods (9.9%). Cutaneous symptoms were most common in both CMA and EWA, and anaphylaxis was noticed in 36.1% and 30.3%, respectively. Baked goods containing milk or eggs also induced anaphylaxis. The symptom onset time was less than 30 minutes in the majority of patients and the most common place of occurrence was home in both CMA and EWA. Conclusion: This study provides comprehensive information on CMA and EWA, and therefore helps clinicians diagnose and guide appropriate food restriction in children with CMA and EWA. (Allergy Asthma Respir Dis 2017;5:351-357)