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신증후군으로 발현한 Light Chain Nephropathy 1예
진성림,손홍주,노승현,고행일 인제대학교 1998 仁濟醫學 Vol.19 No.2
Light Chain Nephropathy는 B 임파구의 비정상적인 클론 증식에 의하여 Light Chain의 과생산과 사구체 및 신세뇨관 기저막에 따라 침착됨으로 임상적으로 단백뇨, 고혈압, 신증후군, 진행하는 신부전을 특징으로 하는 드문 질환으로서 저자들은 신증후군과 고혈압의 임상 증상으로 발현한 Light Chain Nephropathy 1예를 경험하였기에 문헌고찰과 함께 보고하는 바이다. Light chain nephropathy. also called monoclonal immunoglobulin deposition disease, is uncommon disorder in which deposits of monoclonal Ig light chain is found with the glomerular and tubular basement membrane. We experienced a case of light chain nephropathy, was manifested as hypertension, massive proteinuria, and microscopic hematuria in a 60-year old male patient. M-spike is observed in γ-globulin region by the patient's serum immunoelectrophoresis and abnormal dense bands are seen in Ig A and λ-light chain lane by serum protein immunoelectrophoresis. The patient's renal biopsy showed nodular glomerulosclerosis on light microscopy. So we present this case with the revlew of literatures.
진성림,하태완,손홍주,한성훈,정재면,이윤우 인제대학교 1998 仁濟醫學 Vol.19 No.1
당뇨병성 뇌 단신경병증 중에서 가장 흔한 형태는 동안신경의 마비이며 안검하수 및 안구 운동 제한을 보이는데 비해서, 동공의 크기 및 대광반사는 정상을 유지하는 것이 특징이다. 저자들은 양측 측두부 두통과 우측의 안검하수를 주소로 내원한 59세의 여자 환자에서 동안신경 마비의 원인이 동안신경에 가해지는 외부적인 압력에 의한 것이 아니고, 당뇨병성 뇌 단신경병증에 기인한 것임이 밝혀졌기에 문헌 고찰과 함께 보고하는 바이다. Oculomotor nerve palsy is the most common cranial mononeuropathy in diabetes mellitus. The onset is usually abrupt with painful ophthalmoplegia. Pupillary sparing is a single feature of diabetic third nerve palsy, and is occured in most of the cases. This finding has been widely used to distinguish diabetic oculomotor palsy from extrinsic compresive lesions of the third nerve, the latter tending to affect pupillary function first. We experienced a 59-year old diabetic woman with right eye ptosis and headache. The patient showed sparing of papillary reflex and MRI of brain was normal. We present this case with review of literatures.
거대 십이지장 브루너선종의 Detachable Snare 를 이용한 제거 1예
김희숙,박재선,진성림,문정섭,유권,전영빈,손홍주,안진철 대한소화기내시경학회 1998 Clinical Endoscopy Vol.18 No.2
Duodenal Brunner's gland adenoma is characterized by hyperplasia of the Brunner's gland, which is usually found in a duodenal bulb as a pedunculated polypoid mass. Conservative management is advocated for asymptomatic small lesions, but in larger lesions causing obstructive symptoms or bleeding, either endoscopic or surgical removal of the mass should be performed. But an endoscopic polypectomy for a huge mass lesion, especially one having a broad base, runs the risk of bleeding, so to minimize this complication, detachable snare is used before the polypectomy. We have experienced a case of huge duodenal Brunner's gland adenoma was successfully removed by an endoscopic polypectomy with a detachable snare, in a patient with recurrent upper gastrointestinal bleeding.