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양측 원위부 상지를 비대칭적으로 침범한 연소성 근위축증 1예: Hirayama 병
방희제 대한근전도전기진단의학회 2008 대한근전도 전기진단의학회지 Vol.10 No.1
We report a 17-year-old man, who had been showing progressive weakness in right forearm and hand for the last 6 months. Nerve conduction studies showed no specific abnormal finding on motor and sensory nerve of both upper and lower extremities. Electromyography of both upper limbs showed significant evidences of denervation in the both flexor carpi radialis, extensor carpi radialis, triceps brachii, extensor indicis proprius, abductor pollicis brevis, and first dorsal interossei. Both brachioradialis and biceps brachii muscles were not affected. Cervical magnetic resonance imaging (MRI) revealed atrophy of the lower cervical cord in a neutral position of neck and a forward displacement of the dural sac with an expanded venous plexus in a flexed position. We present a Korean case of juvenile muscular atrophy suggesting Hirayama disease with its typical clinical, electrophysiological and neuroradiological findings.
제4, 5 요추 추간판 탈출증에 의한 제 5 요수 신경근병증의 침근전도 양상
황찬호,방희제,이경무,권인수,김호중,박현식 대한근전도전기진단의학회 2009 대한근전도 전기진단의학회지 Vol.11 No.2
Objectives: To determine selecting ideal muscles in evaluating L5 radiculopathy through electrophysiologic study. Methods: Electrophysiologic cases which were confirmed for L5 radiculopathies were studied, excluding peripheral neuropathy other than L5 radiculopathy, myelopahty or recent spine surgery less than 3 years. Twenty-seven patients presented with clinical findings of L5 radiculopathy included. The clinical diagnosis of L5 radiculopathy and intervertebral disc displacement in the 4th and 5th lumbar level was confirmed by magnetic resonance imaging (MRI). Patients with peripheral neuropathy other than L5 radiculopathy, myelopathy or recent spine surgery less than 3 years were excluded. We performed electrophysiologic studies in muscles defined by two different categories: paravertebral, proximal and distal groups. Results: Muscles of extensor hallucis longus (79%), extensor digitorum longus (75%), tibialis anterior (70%), paravertebral muscle (62%), peroneus longus (62%), tensor fascia lata (60%), gluteus medius (38%) and lateral head of gastrocnemius (33%) showed abnormal findings in needle electromyography. Including even one abnormal finding in any muscle in each group, the distal group showed the highest rate of abnormalities such as 100% whereas proximal and paravertebral group showed each rate as 68% and 65% in order. Tensor fascia lata muscle and extensor hallucis longus muscle showed the highest rate of abnormalities in each group. Conclusion: We propose that tensor fascia lata in proximal and extensor hallucis longus in distal muscle groups should be selected in L5 radiculopathy.