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정상 면역기능을 가진 소아에서 수두 감염 후에 발생한 급성 췌장염 1예
오기원,김준성,김자형,박상규,정진영,Oh, Ki-Won,Kim, Joon-Sung,Kim, Ja-Hyeong,Park, Sang-Kyu,Jeong, Jin-Young 대한소아소화기영양학회 2008 Pediatric gastroenterology, hepatology & nutrition Vol.11 No.1
저자들은 복통과 반복적인 구토를 주소로 내원한 정상적인 면역기능을 가진 6세 소아에서 수두-대상포진 바이러스 감염 후에 드문 합병증의 하나로 발생한 급성 췌장염 1예를 경험하였기에 문헌 고찰과 함께 보고하는 바이다. Blunt trauma, drugs, infection, congenital anomalies of the pancreaticobiliary system, and multisystem diseases are the main causes of acute pancreatitis in children. Various viruses can cause acute pancreatitis, but varicella-induced pancreatitis is unusual and generally observed in adults or immunocompromised patients. We report a rare case of acute pancreatitis associated with varicella-zoster virus infection in a 6-year-old immunocompetent girl. The patient initially presented complaining of severe abdominal pain and repetitive vomiting. The patient had multiple cutaneous crusts that has been caused by preceding varicella infection and had elevated values of serum amylase and lipase. Abdominal ultrasonography demonstrated swelling of the pancreas and pancreatic duct dilatation, findings which were compatible with acute pancreatitis. The patient's clinical and laboratory abnormalities were completely normalized through conservative treatment consisting of fasting, total parenteral nutrition, and analgesic therapy.
IL-13 +2044G/A Polymorphism 과 소아천식의 관련성 및 그 기능 연구
김효빈 ( Hyo Bin Kim ),이소연 ( So Yeon Lee ),진현승 ( Hyun Seung Jin ),김자형 ( Ja Hyeong Kim ),김봉성 ( Bong Seong Kim ),강미진 ( Mi Jin Kang ),장성옥 ( Seong Ok Jang ),홍수종 ( Soo Jong Hong ) 대한천식알레르기학회 2006 천식 및 알레르기 Vol.26 No.4
Background: The IL-13 +2044G/A is known to be associated with increased serum total IgE levels and asthma development. Variant type of IL-13 was significantly more active than wild type in inducing CD23 expression in monocytes. Objective: We investigated the association of asthma susceptibility and asthma-related phenotypes with +2044G/A and the functional difference between wild (+2044G, R110) and variant types (+2044A, Q110). Method: We enrolled 358 atopic asthmatic, 81 non-atopic asthmatic, and 146 control children and evaluated total IgE and bronchial hyperresponsiveness. Genotypes were analyzed by PCR-RFLP method. We applied wild and variant types of IL-13 to B cells and evaluated CD23 expression by flow cytometry. Result: The group with more than one variant alleles of +2044G/A was associated with asthma development, but not with increased total IgE levels than those with wild homozygote in children with asthma. When Q110 was applied to peripheral blood B cells of normal subjects and EBV-transformed B cells from children with atopic asthma, CD23 expressions was higher than those when R110 applied. Conclusion: IL-13 +2044G/A was associated with asthma development in Korean children with asthma, but not with total IgE. In addition, Q110 enhanced CD23 expression on B cells. These findings suggest that IL-13 +2044A (Q110) polymorphism may play a role in asthma development or IgE production. (Korean J Asthma Allergy Clin Immunol 2006;26:271-276)
급성 이완성 마비 증상을 보인 엔테로바이러스 71 감염
김현경(Hyun Kyung Kim),이강원(Kang Won Rhee),이경연(Kyung Yeon Lee),오기원(Ki Won Oh),김자형(Ja Hyeong Kim),정진영(Jin Young Jeong),박상규(Sang Kyu Park),최성훈(Seong Hoon Choi) 대한소아신경학회 2011 대한소아신경학회지 Vol.19 No.1
수족구병은 손, 발 및 구강 내 특징적 피부 병변을 보이며 대부분 1주일 내에 저절로 호전되는 질환이지만, EV71 감염으로 인한 수족구병의 경우에는 뇌간 뇌염, 급성 이완성 마비, 뇌수막염 등의 신경학적 합병증이 발생할 수 있으며, 일부에서는 심폐 부전으로 사망에까지 이를 수 있다. 저자들은 18개월 여아에서 수족구병과 동반하여 우측 하지의 급성 이완성 마비 증상을 보인 증례를 경험하였기에 문헌고찰과 함께 보고하는 바이다. Hand-foot-mouth disease (HFMD) is characterized by distinctive skin lesions on the hand, foot, and mouth and in general, recovery occurs within one week. However, in cases of L-HFMD by enterovirus 71 (EV71) infection, the development of neurologic complications such as brainstem encephalitis, acute flaccid paralysis, and aseptic meningitis has been common. Moreover, it has been reported that some patients with neuologic complications have expired in severe cases. Here, we report a case of EV71 infection presented with acute flaccid paralysis of a single similar to paralytic poliomyelitis.
로영아,김성진,이유경,김자형,Ro, Yeong A,Kim, Seong Jin,Lee, Yu Gyeong,Kim, Ja Hyeong Korean Chemical Society 2001 Bulletin of the Korean Chemical Society Vol.22 No.11
Pseudotetragonal ZrO0.75S whose space group is P212121 was synthesized and the cell dimensions were a=5.110(2) $\AA$, b=5.110(7) $\AA$, and c=5.198(8) $\AA.$ The space group P212121 seems to be resulted from lowering the symmetry of cubic ZrOS structure with P213 space group by lattice distortion due to the oxygen defects. In the distorted structure, bond shortening between metal-nonmetal by reduction of cell volume and alternation of Zr-Zr distance were observed. Dielectric constant and loss data of the bulk material in temperature range -170 to 20 $^{\circ}C$ and frequency range 50 Hz to 1 MHz showed that there was dielectric transition at around -70 $^{\circ}C$ originated from the relaxation of Zr-S segment. Comparing with ZrO2 exhibited the dielectirc constants, 9.0 at room temperature, ZrO0.75S showed high dielectric constant, k = 200.2 at 100 kHz. The activation energy of relaxation time due to dielectric relaxation of Zr-S was 0.47 eV (11.3 kcal/mole). According to the impedance spectra, ZrO0.75S showed more parallel circuit character between the resistance and capacitance components at the temperature (-70 $^{\circ}C)$ that the Zr-S dielectric relaxation was observed.
저혈당성 경련으로 내원한 환자에서 진단된 Silver-Russell 증후군 1례
이정용(Jung Yong Lee)ㆍ김영아(Young A Kim)ㆍ이경연(Kyung Yeon Lee)ㆍ오기원(Ki Won Oh)ㆍ김자형(Ja Hyeong Kim)ㆍ김준성(Joon Sung Kim)ㆍ정진영(Jin Young Jeong)ㆍ박상규(Sang Kyu Park) 대한소아신경학회 2010 대한소아신경학회지 Vol.18 No.1
저자들은 저혈당성 경련을 주소로 내원한 4세 여아에서 자궁 내 성장 지연, 출생 후 지속되는 저신장과 저체중, 몸에 비해 상대적으로 큰 머리, 신체의좌우 비대칭, 특징적인 얼굴 모양을 보인 Silver-Russell 증후군 1례를 경험하였기에 문헌 고찰과함께 보고하는 바이다. The Silver-Russell syndrome(SRS) is a clinically heterogeneous syndrome characterized by intrauterine and postnatal growth retardation with spared cranial growth, characteristic facial features, and body asymmetry. Although mild to moderate hypoglycemic symptoms occasionally appear in children with SRS especially those who are not fed frequently and regularly, hypoglycemic seizures rarely occur. We report a rare case of SRS which was diagnosed in a 4-year-old female who admitted with hypoglycemic seizure. The patient showed the haracteristic features of SRS. Endocrinologic studies were normal except for partial growth hormone insufficiency. To prevent seizures and chronic neurologic deficits in children with SRS, the early recognition and appropriate management of hypoglycemia is critical.
오기원 ( Ki Won Oh ),이경연 ( Kyung Yeon Lee ),김자형 ( Ja Hyeong Kim ),김준성 ( Joon Sung Kim ) 대한주산의학회 2012 Perinatology Vol.23 No.1
Umbilical catheterization is one of the common procedures performed in the neonatal intensive care unit, but it is sometimes associated with significant complications. Atrial flutter (AF) is a rare cardiac complication following the insertion of an umbilical venous catheter. We report a newborn infant who developed AF after umbilical venous catheterization. The tachyarrhythmia was successfully managed with synchronized cardiover sion. There were no recurrent episodes of AF and antiarrhythmic medications were not needed on the follow-up.
중증 아토피피부염 환아에서 Cyclosporine 치료 후 T세포의 변화
이소연 ( Lee So Yeon ),박진호 ( Park Jin Ho ),심정연 ( Sim Jeong Yeon ),김자형 ( Kim Ja Hyeong ),김봉성 ( Kim Bong Seong ),서지혜 ( Seo Ji Hye ),장성옥 ( Jang Seong Og ),홍수종 ( Hong Su Jong ) 대한소아알레르기호흡기학회(구 대한소아알레르기 및 호흡기학회) 2004 소아알레르기 및 호흡기학회지 Vol.14 No.1
목적: 중증의 아토피피부염 치료에 비교적 안전하게 쓰이는 cyclosporine은 활성화된 T림프구와 T림프구에서 생성하는 사이토카인을 조절하는데 아토피피부염에서의 정확한 기전은 밝혀진 바가 적다. 표피 림프구 항원 (cutaneous lymphocyte antigen, CLA)을 발현하는 skin-homing 기억 T림프구는 아토피피부염의 병인에 있어서 중요한 역할을 하는데, cyclosporine 치료 전후로 이러한 CLA+T 림프구의 변화를 보고자 Background: Skin-homing T cells expressing cutaneous lymphocyte antigen (CLA) are known to be important in the pathogenesis of atopic dermatitis (AD). Cyclosporine is known as an effective treatment for severe atopic dermatitis, which controls the cytokin
천식과 알레르기비염을 가진 초등학생의 행동 특성과 부모의 양육 스트레스
최은정 ( Eunjeong Choi ),이미지 ( Mi Ji Lee ),윤현진 ( Hyun-jin Yun ),김자형 ( Ja Hyeong Kim ),이주석 ( Ju Suk Lee ),박재홍 ( Jae Hong Park ),정진아 ( Jin-a Jung ) 대한천식알레르기학회 2016 Allergy Asthma & Respiratory Disease Vol.4 No.3
Purpose: The aim of this study was to investigate the differences in behavioral characteristics and parental stress between allergic and nonallergic elementary school children. Methods: Ninety-one elementary school children who had allergic disease were enrolled (asthma, n=27; allergic rhinitis, n=35; combined, n=29). Also one hundred six nonallergic elementary school children were enrolled for the control group. The Korean Child Behavior Check List (K-CBCL) and Korean Parenting Stress Index-Short Form (K-PSI-SF) were completed by their mothers. Results: According to the analysis of K-CBCL, the score for Internalizing, anxious/depressed and somatic complaints were significantly higher in the combined group than in the control group. The score for Diagnostic and Statistical Manual of Mental Disorders (DSM)-affective problems in the combined group and DSM-somatic problems were significantly higher in the asthma group than in the control group. According to the analysis of K-PSI-SF, the score for parental distress was significantly higher in the allergic rhinitis group than in the control group. The scores for behavioral problems and parental stress were significantly correlated to allergic disease groups. Conclusion: Behavioral problems and parental stress were significantly associated with asthma and allergic rhinitis. The results of this study suggest the importance of psychosocial support for mothers and children with allergic diseases. (Allergy Asthma Respir Dis 2016;4:205-211)